No amelioration of uromodulin maturation and trafficking defect by sodium 4-phenylbutyrate in vivo: studies in mouse models of uromodulin-associated kidney disease.
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Uromodulin retention in thick ascending limb of Henle's loop affects SCD1 in neighboring proximal tubule: renal transcriptome studies in mouse models of uromodulin-associated kidney diseaseMutant uromodulin expression leads to altered homeostasis of the endoplasmic reticulum and activates the unfolded protein response.Mitochondrial Dysregulation Secondary to Endoplasmic Reticulum Stress in Autosomal Dominant Tubulointerstitial Kidney Disease - UMOD (ADTKD-UMOD)Uromodulin: from monogenic to multifactorial diseases.Uromodulin: from physiology to rare and complex kidney disorders.Early involvement of cellular stress and inflammatory signals in the pathogenesis of tubulointerstitial kidney disease due to UMOD mutations.Endoplasmic reticulum stress, the unfolded protein response and autophagy in kidney diseases.
P2860
Q27324759-20D1DBAE-5A9B-4ECD-B1FA-171292E0158BQ36355151-B88BC393-AA05-498B-97E5-478D5083F14AQ37655066-9002F7D1-BDFA-435D-BDFA-F04BCF95FDC2Q38250313-B44CD2F4-0861-44B5-B3D6-3F5C81DD3C34Q38638219-75736E22-9ACC-4665-8ED9-6BAA09D04183Q41287767-442AE34B-65A1-47FB-AC6D-2B1DD6FCA8CAQ47711878-3A1C4AB5-0297-4D28-A55F-A062FF3C35B8
P2860
No amelioration of uromodulin maturation and trafficking defect by sodium 4-phenylbutyrate in vivo: studies in mouse models of uromodulin-associated kidney disease.
description
2014 nî lūn-bûn
@nan
2014年の論文
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2014年学术文章
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2014年学术文章
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2014年学术文章
@zh-hans
2014年学术文章
@zh-my
2014年学术文章
@zh-sg
2014年學術文章
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2014年學術文章
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2014年學術文章
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name
No amelioration of uromodulin ...... lin-associated kidney disease.
@en
No amelioration of uromodulin ...... lin-associated kidney disease.
@nl
type
label
No amelioration of uromodulin ...... lin-associated kidney disease.
@en
No amelioration of uromodulin ...... lin-associated kidney disease.
@nl
prefLabel
No amelioration of uromodulin ...... lin-associated kidney disease.
@en
No amelioration of uromodulin ...... lin-associated kidney disease.
@nl
P2860
P50
P356
P1476
No amelioration of uromodulin ...... ulin-associated kidney disease
@en
P2093
Birgit Rathkolb
Stefanie Sklenak
P2860
P304
10715-10726
P356
10.1074/JBC.M113.537035
P407
P577
2014-02-24T00:00:00Z