The activator of cerebroside sulphatase. Purification from human liver and identification as a protein.
about
Saposin A: second cerebrosidase activator proteinCharacterization of a mutation in a family with saposin B deficiency: a glycosylation site defectAB variant of infantile GM2 gangliosidosis: deficiency of a factor necessary for stimulation of hexosaminidase A-catalyzed degradation of ganglioside GM2 and glycolipid GA2The protective role of prosaposin and its receptors in the nervous systemPresence of activator proteins for the enzymic hydrolysis of GM1 and GM2 gangliosides in normal human urineGenetic heterogeneity in metachromatic leukodystrophyBiosynthesis and degradation of mammalian glycosphingolipids.Cerebroside sulfatase activator deficiency induced metachromatic leukodystrophy.Placental steroid deficiency: association with arylsulfatase A deficiency.Ganglioside GM2 N-acetyl-beta-D-galactosaminidase activity in cultured fibroblasts of late-infantile and adult GM2 gangliosidosis patients and of healthy probands with low hexosaminidase level.Interaction of activating protein and surfactants with human liver hexosaminidase A and GM2 ganglioside.Purification and properties of the hexosaminidase A-activating protein from human liver.Inheritance of metachromatic leukodystrophy.Membrane-spanning lipids for an uncompromised monitoring of membrane fusion and intermembrane lipid transfer.Progranulin-mediated deficiency of cathepsin D results in FTD and NCL-like phenotypes in neurons derived from FTD patients.
P2860
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P2860
The activator of cerebroside sulphatase. Purification from human liver and identification as a protein.
description
1975 nî lūn-bûn
@nan
1975年の論文
@ja
1975年論文
@yue
1975年論文
@zh-hant
1975年論文
@zh-hk
1975年論文
@zh-mo
1975年論文
@zh-tw
1975年论文
@wuu
1975年论文
@zh
1975年论文
@zh-cn
name
The activator of cerebroside s ...... d identification as a protein.
@en
type
label
The activator of cerebroside s ...... d identification as a protein.
@en
prefLabel
The activator of cerebroside s ...... d identification as a protein.
@en
P1476
The activator of cerebroside s ...... d identification as a protein.
@en
P2093
Jatzkewitz H
P304
P577
1975-05-01T00:00:00Z