Activation of deltaF508 CFTR in a cystic fibrosis respiratory epithelial cell line by 4-phenylbutyrate, genistein and CPX.
about
Digitoxin mimics gene therapy with CFTR and suppresses hypersecretion of IL-8 from cystic fibrosis lung epithelial cellsClinical and experimental applications of sodium phenylbutyrateClinical and pharmacological experience with LJP-394.Physical Characterization of 1,3-dipropyl-8-cyclopentylxanthine (CPX).Disease-causing missense mutations in actin binding domain 1 of dystrophin induce thermodynamic instability and protein aggregation.Pharmacological treatment of the ion transport defect in cystic fibrosis.Cystic fibrosis bronchial epithelial cells are lipointoxicated by membrane palmitate accumulation.Emerging drug treatments for cystic fibrosis.Pharmacological approaches to correcting the ion transport defect in cystic fibrosis.Toward the pharmacogenomics of cystic fibrosis--an update.Natural Compounds as Therapeutic Agents in the Treatment Cystic FibrosisFront-runners for pharmacotherapeutic correction of the airway ion transport defect in cystic fibrosis.Trafficking of GFP-tagged DeltaF508-CFTR to the plasma membrane in a polarized epithelial cell line.Cystic fibrosis transmembrane conductance regulator differentially regulates human and mouse epithelial sodium channels in Xenopus oocytes.Genistein improves regulatory interactions between G551D-cystic fibrosis transmembrane conductance regulator and the epithelial sodium channel in Xenopus oocytes.A phase I randomized, multicenter trial of CPX in adult subjects with mild cystic fibrosis.Use of nasal potential difference and sweat chloride as outcome measures in multicenter clinical trials in subjects with cystic fibrosis.The effect of ambroxol on chloride transport, CFTR and ENaC in cystic fibrosis airway epithelial cells.Modulation of deltaF508 cystic fibrosis transmembrane regulator trafficking and function with 4-phenylbutyrate and flavonoids.Nutraceutical-mediated restoration of wild-type levels of IKBKAP-encoded IKAP protein in familial dysautonomia-derived cells.
P2860
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P2860
Activation of deltaF508 CFTR in a cystic fibrosis respiratory epithelial cell line by 4-phenylbutyrate, genistein and CPX.
description
2000 nî lūn-bûn
@nan
2000年の論文
@ja
2000年学术文章
@wuu
2000年学术文章
@zh-cn
2000年学术文章
@zh-hans
2000年学术文章
@zh-my
2000年学术文章
@zh-sg
2000年學術文章
@yue
2000年學術文章
@zh
2000年學術文章
@zh-hant
name
Activation of deltaF508 CFTR i ...... ylbutyrate, genistein and CPX.
@en
type
label
Activation of deltaF508 CFTR i ...... ylbutyrate, genistein and CPX.
@en
prefLabel
Activation of deltaF508 CFTR i ...... ylbutyrate, genistein and CPX.
@en
P1476
Activation of deltaF508 CFTR i ...... ylbutyrate, genistein and CPX.
@en
P2093
C Andersson
G M Roomans
P304
P356
10.1034/J.1399-3003.2000.15E21.X
P577
2000-05-01T00:00:00Z