Aberrant development of neuromuscular junctions in glycosylation-defective Large(myd) mice.
about
To build a synapse: signaling pathways in neuromuscular junction assemblyTransgenic overexpression of LARGE induces α-dystroglycan hyperglycosylation in skeletal and cardiac muscleMuscle-specific expression of LARGE restores neuromuscular transmission deficits in dystrophic LARGE(myd) miceCLP1 links tRNA metabolism to progressive motor-neuron loss.Clinical, pathologic, and mutational spectrum of dystroglycanopathy caused by LARGE mutations.Protein O-mannosylation in animal development and physiology: from human disorders to Drosophila phenotypesAutologous intramuscular transplantation of engineered satellite cells induces exosome-mediated systemic expression of Fukutin-related protein and rescues disease phenotype in a murine model of limb-girdle muscular dystrophy type 2I.
P2860
Q24631081-01A618E8-A680-4E1F-B955-2D5216DC3BE7Q33784310-E2DFA971-D013-4511-BD2B-8F85319ADFAAQ36559993-EC3DA96B-FAAC-44DC-8CEB-07F9CE108536Q36907351-41DF2D88-6544-4B85-97B3-CA240DFEE060Q37420817-757FDD17-038E-400A-98DA-E846A5D1BCBBQ37723603-D2952CD9-9D3C-4AF2-B0C6-E51479878F22Q47969705-99BBB0C0-BF23-4A58-973B-44285FBAE80A
P2860
Aberrant development of neuromuscular junctions in glycosylation-defective Large(myd) mice.
description
2009 nî lūn-bûn
@nan
2009年の論文
@ja
2009年論文
@yue
2009年論文
@zh-hant
2009年論文
@zh-hk
2009年論文
@zh-mo
2009年論文
@zh-tw
2009年论文
@wuu
2009年论文
@zh
2009年论文
@zh-cn
name
Aberrant development of neuromuscular junctions in glycosylation-defective Large
@nl
Aberrant development of neurom ...... ion-defective Large(myd) mice.
@en
type
label
Aberrant development of neuromuscular junctions in glycosylation-defective Large
@nl
Aberrant development of neurom ...... ion-defective Large(myd) mice.
@en
prefLabel
Aberrant development of neuromuscular junctions in glycosylation-defective Large
@nl
Aberrant development of neurom ...... ion-defective Large(myd) mice.
@en
P2860
P1476
Aberrant development of neurom ...... tion-defective Large(myd) mice
@en
P2093
Ewald Unger
Reginald E Bittner
P2860
P304
P356
10.1016/J.NMD.2009.02.011
P577
2009-04-05T00:00:00Z