Overexpression of mini-agrin in skeletal muscle increases muscle integrity and regenerative capacity in laminin-alpha2-deficient mice.
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Skeletal muscle laminin and MDC1A: pathogenesis and treatment strategies.Apoptosis inhibitors and mini-agrin have additive benefits in congenital muscular dystrophy miceDevelopmental and pathogenic mechanisms of basement membrane assemblyDistinct roles for laminin globular domains in laminin alpha1 chain mediated rescue of murine laminin alpha2 chain deficiencyHanging on for the ride: adhesion to the extracellular matrix mediates cellular responses in skeletal muscle morphogenesis and diseaseNAD+ biosynthesis ameliorates a zebrafish model of muscular dystrophy.Laminin alpha1 chain mediated reduction of laminin alpha2 chain deficient muscular dystrophy involves integrin alpha7beta1 and dystroglycan.Extrinsic regulation of satellite cell specificationMuscle-specific expression of insulin-like growth factor 1 improves outcome in Lama2Dy-w mice, a model for congenital muscular dystrophy type 1AProinflammatory signals and the loss of lymphatic vessel hyaluronan receptor-1 (LYVE-1) in the early pathogenesis of laminin alpha2-deficient skeletal muscle.Interactions between Skeletal Muscle Myoblasts and their Extracellular Matrix Revealed by a Serum Free Culture System.Meeting Report: New Directions in the Biology and Disease of Skeletal Muscle 2014PEDF-derived peptide promotes skeletal muscle regeneration through its mitogenic effect on muscle progenitor cellsOverexpression of the cytotoxic T cell (CT) carbohydrate inhibits muscular dystrophy in the dyW mouse model of congenital muscular dystrophy 1A.Laminin-111 protein therapy reduces muscle pathology and improves viability of a mouse model of merosin-deficient congenital muscular dystrophyMesoangioblast delivery of miniagrin ameliorates murine model of merosin-deficient congenital muscular dystrophy type 1A.Linker molecules between laminins and dystroglycan ameliorate laminin-alpha2-deficient muscular dystrophy at all disease stagesRole of extracellular matrix proteins and their receptors in the development of the vertebrate neuromuscular junctionFibronectin regulates Wnt7a signaling and satellite cell expansionLaminin-211 in skeletal muscle function.The emerging biology of muscle stem cells: implications for cell-based therapies.Adeno-associated viral-mediated LARGE gene therapy rescues the muscular dystrophic phenotype in mouse models of dystroglycanopathy.Overexpression of Galgt2 reduces dystrophic pathology in the skeletal muscles of alpha sarcoglycan-deficient mice212th ENMC International Workshop: Animal models of congenital muscular dystrophies, Naarden, The Netherlands, 29-31 May 2015.Vascular delivery of rAAVrh74.MCK.GALGT2 to the gastrocnemius muscle of the rhesus macaque stimulates the expression of dystrophin and laminin α2 surrogates.Cell-matrix interactions in muscle disease.A Novel Egr-1-Agrin Pathway and Potential Implications for Regulation of Synaptic Physiology and Homeostasis at the Neuromuscular JunctionLaminin: loss-of-function studies.B4GALNT2 (GALGT2) Gene Therapy Reduces Skeletal Muscle Pathology in the FKRP P448L Mouse Model of Limb Girdle Muscular Dystrophy 2I.Angiotensin II type 1 receptor antagonists alleviate muscle pathology in the mouse model for laminin-α2-deficient congenital muscular dystrophy (MDC1A).Laminin-111 improves muscle repair in a mouse model of merosin-deficient congenital muscular dystrophy.Hedgehog signaling and laminin play unique and synergistic roles in muscle development.Transgenic overexpression of the α7 integrin reduces muscle pathology and improves viability in the dy(W) mouse model of merosin-deficient congenital muscular dystrophy type 1A.Dysregulation of matricellular proteins is an early signature of pathology in laminin-deficient muscular dystrophy.ECM-Related Myopathies and Muscular Dystrophies: Pros and Cons of Protein Therapies.Linker proteins restore basement membrane and correct LAMA2-related muscular dystrophy in mice.Laminin-deficient muscular dystrophy: Molecular pathogenesis and structural repair strategies.Muscular dystrophy meets protein biochemistry, the mother of invention.Laminin-521 Protein Therapy for Glomerular Basement Membrane and Podocyte Abnormalities in a Model of Pierson Syndrome.Amelioration of Muscle and Nerve Pathology in LAMA2 Muscular Dystrophy by AAV9-Mini-Agrin.
P2860
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P2860
Overexpression of mini-agrin in skeletal muscle increases muscle integrity and regenerative capacity in laminin-alpha2-deficient mice.
description
2005 nî lūn-bûn
@nan
2005年の論文
@ja
2005年論文
@yue
2005年論文
@zh-hant
2005年論文
@zh-hk
2005年論文
@zh-mo
2005年論文
@zh-tw
2005年论文
@wuu
2005年论文
@zh
2005年论文
@zh-cn
name
Overexpression of mini-agrin i ...... laminin-alpha2-deficient mice.
@en
Overexpression of mini-agrin i ...... laminin-alpha2-deficient mice.
@nl
type
label
Overexpression of mini-agrin i ...... laminin-alpha2-deficient mice.
@en
Overexpression of mini-agrin i ...... laminin-alpha2-deficient mice.
@nl
prefLabel
Overexpression of mini-agrin i ...... laminin-alpha2-deficient mice.
@en
Overexpression of mini-agrin i ...... laminin-alpha2-deficient mice.
@nl
P2093
P356
P1433
P1476
Overexpression of mini-agrin i ...... laminin-alpha2-deficient mice
@en
P2093
Markus A Ruegg
Patrizia Barzaghi
P304
P356
10.1096/FJ.04-3376COM
P407
P577
2005-06-01T00:00:00Z