Direct visualization of the dystrophin network on skeletal muscle fiber membrane.
about
Specific interaction of the actin-binding domain of dystrophin with intermediate filaments containing keratin 19.Muscle regeneration in dystrophin-deficient mdx mice studied by gene expression profilingThe dystrophin complex forms a mechanically strong link between the sarcolemma and costameric actinAssociation of aciculin with dystrophin and utrophinBeta 1D integrin displaces the beta 1A isoform in striated muscles: localization at junctional structures and signaling potential in nonmuscle cellsBiomechanics of the sarcolemma and costameres in single skeletal muscle fibers from normal and dystrophin-null miceIsolation and characterization of distinct domains of sarcolemma and T-tubules from rat skeletal muscleL-type Ca2+ channel function is linked to dystrophin expression in mammalian muscleDystrophic Cardiomyopathy-Potential Role of Calcium in Pathogenesis, Treatment and Novel TherapiesSarcolemmal organization in skeletal muscle lacking desmin: evidence for cytokeratins associated with the membrane skeleton at costameres.Disease-causing missense mutations in actin binding domain 1 of dystrophin induce thermodynamic instability and protein aggregation.Ultrastructural localization of the C-terminus of the 43-kd dystrophin-associated glycoprotein and its relation to dystrophin in normal murine skeletal myofiber.Transgenic mdx mice expressing dystrophin with a deletion in the actin-binding domain display a "mild Becker" phenotype.Animal models for muscular dystrophy show different patterns of sarcolemmal disruption.Extensive but coordinated reorganization of the membrane skeleton in myofibers of dystrophic (mdx) mice.Challenges and opportunities in dystrophin-deficient cardiomyopathy gene therapy.In vivo gene editing in dystrophic mouse muscle and muscle stem cells.Dystrophin and utrophin have distinct effects on the structural dynamics of actinCardiac and respiratory dysfunction in Duchenne muscular dystrophy and the role of second messengers.Aquaporin 4 Expression in the mdx Mouse DiaphragmABC of multifaceted dystrophin glycoprotein complex (DGC).Disruption of sarcolemmal dystrophin and beta-dystroglycan may be a potential mechanism for myocardial dysfunction in severe sepsis.The carboxy-terminal third of dystrophin enhances actin binding activity.Dystrophin isoforms DP71 and DP427 have distinct roles in myogenic cells.Dystrophin and its isoforms.Interaction of dystrophin fragments with model membranesMuscle activity and muscle agrin regulate the organization of cytoskeletal proteins and attached acetylcholine receptor (AchR) aggregates in skeletal muscle fibers.Cultured rat skeletal muscle cells treated with cytochalasin exhibit normal dystrophin expression and intracellular free calcium control.Ischemic preconditioning-mediated restoration of membrane dystrophin during reperfusion correlates with protection against contraction-induced myocardial injury.Predictive model identifies key network regulators of cardiomyocyte mechano-signaling.Temporary blockade of contractility during reperfusion elicits a cardioprotective effect of the p38 MAP kinase inhibitor SB-203580.Identification of spectrin-like repeats required for high affinity utrophin-actin interaction.Co-localization of dystrophin and beta-dystroglycan demonstrated in en face view by double immunogold labeling of freeze-fractured skeletal muscle.Administration of chinese herbal medicines facilitates the locomotor activity in dystrophin-deficient mice.
P2860
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P2860
Direct visualization of the dystrophin network on skeletal muscle fiber membrane.
description
1992 nî lūn-bûn
@nan
1992年の論文
@ja
1992年論文
@yue
1992年論文
@zh-hant
1992年論文
@zh-hk
1992年論文
@zh-mo
1992年論文
@zh-tw
1992年论文
@wuu
1992年论文
@zh
1992年论文
@zh-cn
name
Direct visualization of the dystrophin network on skeletal muscle fiber membrane.
@en
Direct visualization of the dystrophin network on skeletal muscle fiber membrane.
@nl
type
label
Direct visualization of the dystrophin network on skeletal muscle fiber membrane.
@en
Direct visualization of the dystrophin network on skeletal muscle fiber membrane.
@nl
prefLabel
Direct visualization of the dystrophin network on skeletal muscle fiber membrane.
@en
Direct visualization of the dystrophin network on skeletal muscle fiber membrane.
@nl
P2093
P2860
P356
P1476
Direct visualization of the dystrophin network on skeletal muscle fiber membrane.
@en
P2093
P2860
P304
P356
10.1083/JCB.119.5.1183
P407
P577
1992-12-01T00:00:00Z