The neuronal migration defect in mice with Zellweger syndrome (Pex5 knockout) is not caused by the inactivity of peroxisomal beta-oxidation.
about
Pathogenesis of peroxisomal deficiency disorders (Zellweger syndrome) may be mediated by misregulation of the GABAergic system via the diazepam binding inhibitorAbsence of peroxisomes in mouse hepatocytes causes mitochondrial and ER abnormalitiesCerebral MRI as a valuable diagnostic tool in Zellweger spectrum patients.Overexpression of peroxisome proliferator-activated receptor-alpha (PPARalpha)-regulated genes in liver in the absence of peroxisome proliferation in mice deficient in both L- and D-forms of enoyl-CoA hydratase/dehydrogenase enzymes of peroxisomal bPeroxisomal multifunctional protein-2 deficiency causes motor deficits and glial lesions in the adult central nervous system.Deletion of a single allele of the Pex11β gene is sufficient to cause oxidative stress, delayed differentiation and neuronal death in mouse brainPeroxisomes, myelination, and axonal integrity in the CNS.Developmental changes of bile acid composition and conjugation in L- and D-bifunctional protein single and double knockout mice.Clinical and biochemical spectrum of D-bifunctional protein deficiency.
P2860
Q21260342-86A789F8-31CD-4761-A6EE-10386913A928Q28508098-C7453DBE-176B-41E3-9762-993028242E50Q31152736-88DC8589-ED56-45AF-9435-5E9F040A0D9AQ34263929-4B610FA7-605E-4F53-BD01-99908BF407E4Q35088180-9FC09497-1B30-4870-AFFF-CCF5064987BCQ35665063-0522F673-A73F-43EF-86BC-D6A5ADB4C92FQ37576855-CD9B92D3-0774-4F2A-AFE1-9347FC8FECE4Q46381090-84CCC831-9970-44BF-A1EE-3B8F90AFA0FFQ48701952-C4F267B2-3C21-42F1-80AD-C314F2F88C79
P2860
The neuronal migration defect in mice with Zellweger syndrome (Pex5 knockout) is not caused by the inactivity of peroxisomal beta-oxidation.
description
2002 nî lūn-bûn
@nan
2002年の論文
@ja
2002年学术文章
@wuu
2002年学术文章
@zh
2002年学术文章
@zh-cn
2002年学术文章
@zh-hans
2002年学术文章
@zh-my
2002年学术文章
@zh-sg
2002年學術文章
@yue
2002年學術文章
@zh-hant
name
The neuronal migration defect ...... of peroxisomal beta-oxidation.
@en
The neuronal migration defect in mice with Zellweger syndrome
@nl
type
label
The neuronal migration defect ...... of peroxisomal beta-oxidation.
@en
The neuronal migration defect in mice with Zellweger syndrome
@nl
prefLabel
The neuronal migration defect ...... of peroxisomal beta-oxidation.
@en
The neuronal migration defect in mice with Zellweger syndrome
@nl
P2093
P2860
P356
P1476
The neuronal migration defect ...... of peroxisomal beta-oxidation.
@en
P2093
G P Mannaerts
P E Declercq
Veldhoven P P Van
P2860
P304
P356
10.1093/JNEN/61.4.368
P577
2002-04-01T00:00:00Z