Phenylalanine hydroxylase misfolding and pharmacological chaperones.
about
Pharmacological chaperoning: a primer on mechanism and pharmacologyProtein homeostasis disorders of key enzymes of amino acids metabolism: mutation-induced protein kinetic destabilization and new therapeutic strategies.A commentary on the utility of a new L-DOPA-responsive dystonia mouse modelProtein homeostasis defects of alanine-glyoxylate aminotransferase: new therapeutic strategies in primary hyperoxaluria type I.Innovative strategies to treat protein misfolding in inborn errors of metabolism: pharmacological chaperones and proteostasis regulators.Molecular genetics and diagnosis of phenylketonuria: state of the art.Protein Stability, Folding and Misfolding in Human PGK1 Deficiency.Genetics of Phenylketonuria: Then and Now.Tyrosine and tryptophan hydroxylases as therapeutic targets in human disease.Structural basis for ligand-dependent dimerization of phenylalanine hydroxylase regulatory domain.Conformational stabilization as a strategy to prevent nucleophosmin mislocalization in leukemia.Natural (and Unnatural) Small Molecules as Pharmacological Chaperones and Inhibitors in Cancer.The Effects of PMM2-CDG-Causing Mutations on the Folding, Activity, and Stability of the PMM2 Protein.Generation of urine-derived induced pluripotent stem cells from a patient with phenylketonuria.Phenylalanine iminoboronates as new phenylalanine hydroxylase modulators
P2860
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P2860
Phenylalanine hydroxylase misfolding and pharmacological chaperones.
description
2012 nî lūn-bûn
@nan
2012 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2012 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2012年の論文
@ja
2012年論文
@yue
2012年論文
@zh-hant
2012年論文
@zh-hk
2012年論文
@zh-mo
2012年論文
@zh-tw
2012年论文
@wuu
name
Phenylalanine hydroxylase misfolding and pharmacological chaperones.
@ast
Phenylalanine hydroxylase misfolding and pharmacological chaperones.
@en
Phenylalanine hydroxylase misfolding and pharmacological chaperones.
@nl
type
label
Phenylalanine hydroxylase misfolding and pharmacological chaperones.
@ast
Phenylalanine hydroxylase misfolding and pharmacological chaperones.
@en
Phenylalanine hydroxylase misfolding and pharmacological chaperones.
@nl
prefLabel
Phenylalanine hydroxylase misfolding and pharmacological chaperones.
@ast
Phenylalanine hydroxylase misfolding and pharmacological chaperones.
@en
Phenylalanine hydroxylase misfolding and pharmacological chaperones.
@nl
P2860
P921
P1476
Phenylalanine hydroxylase misfolding and pharmacological chaperones
@en
P2093
Oscar Aubi
P2860
P304
P356
10.2174/1568026611212220008
P5008
P577
2012-01-01T00:00:00Z