about
Pass the bicarb: the importance of HCO3– for mucin releaseA novel host defense system of airways is defective in cystic fibrosisAnimal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and DivergencesMicroscale imaging of cilia-driven fluid flowGene therapy: light is finally in the tunnelCharacterization of defects in ion transport and tissue development in cystic fibrosis transmembrane conductance regulator (CFTR)-knockout ratsAirway Gland Structure and FunctionProduction of CFTR-null and CFTR-DeltaF508 heterozygous pigs by adeno-associated virus-mediated gene targeting and somatic cell nuclear transferThe Pig: A Relevant Model for Evaluating the Neutrophil Serine Protease Activities during Acute Pseudomonas aeruginosa Lung InfectionBarriers to inhaled gene therapy of obstructive lung diseases: A reviewThe role of the UPS in cystic fibrosis.Very mild disease phenotype of congenic CftrTgH(neoim)Hgu cystic fibrosis miceTissue and cellular expression patterns of porcine CFTR: similarities to and differences from human CFTRLung phenotype of juvenile and adult cystic fibrosis transmembrane conductance regulator-knockout ferrets.Porcine nasal epithelial cultures for studies of cystic fibrosis sinusitisDistribution and size of mucous glands in the ferret tracheobronchial tree.Pathophysiological preconditions promoting mixed "black" pigment plus cholesterol gallstones in a DeltaF508 mouse model of cystic fibrosis.Generation of multipotent lung and airway progenitors from mouse ESCs and patient-specific cystic fibrosis iPSCs.Disease phenotype of a ferret CFTR-knockout model of cystic fibrosis.Completion of the swine genome will simplify the production of swine as a large animal biomedical model.Ferret and pig models of cystic fibrosis: prospects and promise for gene therapy.Coordinated international action to accelerate genome-to-phenome with FAANG, the Functional Annotation of Animal Genomes projectEfficient production of Fah-null heterozygote pigs by chimeric adeno-associated virus-mediated gene knockout and somatic cell nuclear transfer.Cystic fibrosis: an inherited disease affecting mucin-producing organs.Porcine models of digestive disease: the future of large animal translational research.Processing and function of CFTR-DeltaF508 are species-dependent.Chloride secretion by cultures of pig tracheal gland cells.5'-adenosine monophosphate mediated cooling treatment enhances ΔF508-Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) stability in vivo.Murine and human CFTR exhibit different sensitivities to CFTR potentiators.The pig as a model for investigating the role of neutrophil serine proteases in human inflammatory lung diseases.Keratin K18 increases cystic fibrosis transmembrane conductance regulator (CFTR) surface expression by binding to its C-terminal hydrophobic patch.The Peter Pan paradigm.The cystic fibrosis gene: a molecular genetic perspectiveSalt, chloride, bleach, and innate host defense.New animal models of cystic fibrosis: what are they teaching us?Comparative biology of cystic fibrosis animal modelsLoss of Cftr function exacerbates the phenotype of Na(+) hyperabsorption in murine airways.The porcine lung as a potential model for cystic fibrosisAirway acidification initiates host defense abnormalities in cystic fibrosis mice.Disruption of the CFTR gene produces a model of cystic fibrosis in newborn pigs.
P2860
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P2860
description
2006 nî lūn-bûn
@nan
2006年の論文
@ja
2006年論文
@yue
2006年論文
@zh-hant
2006年論文
@zh-hk
2006年論文
@zh-mo
2006年論文
@zh-tw
2006年论文
@wuu
2006年论文
@zh
2006年论文
@zh-cn
name
Cystic fibrosis mouse models.
@ast
Cystic fibrosis mouse models.
@en
type
label
Cystic fibrosis mouse models.
@ast
Cystic fibrosis mouse models.
@en
prefLabel
Cystic fibrosis mouse models.
@ast
Cystic fibrosis mouse models.
@en
P2860
P356
P1476
Cystic fibrosis mouse models.
@en
P2093
Claudine Guilbault
Zienab Saeed
P2860
P356
10.1165/RCMB.2006-0184TR
P577
2006-08-03T00:00:00Z