The hybrid PAX3-FKHR fusion protein of alveolar rhabdomyosarcoma transforms fibroblasts in culture
about
Transcriptional modulation of the anti-apoptotic protein BCL-XL by the paired box transcription factors PAX3 and PAX3/FKHRForkhead homologue in rhabdomyosarcoma functions as a bifunctional nuclear receptor-interacting protein with both coactivator and corepressor functionsThe human forkhead protein FREAC-2 contains two functionally redundant activation domains and interacts with TBP and TFIIBIRIZIO: a novel gene cooperating with PAX3-FOXO1 in alveolar rhabdomyosarcoma (ARMS)Inhibition of nuclear import by protein kinase B (Akt) regulates the subcellular distribution and activity of the forkhead transcription factor AFX.Foxm1b transcription factor is essential for development of hepatocellular carcinomas and is negatively regulated by the p19ARF tumor suppressorPAX3-FOXO1 fusion gene in rhabdomyosarcomaPAX7 expression in embryonal rhabdomyosarcoma suggests an origin in muscle satellite cellsMechanisms of impaired differentiation in rhabdomyosarcomaInducible short-term and stable long-term cell culture systems reveal that the PAX3-FKHR fusion oncoprotein regulates CXCR4, PAX3, and PAX7 expressionConstitutively active FOXO4 inhibits Akt activity, regulates p27 Kip1 stability, and suppresses HER2-mediated tumorigenicityCell-type-specific regulation of distinct sets of gene targets by Pax3 and Pax3/FKHRStructural and functional studies of FKHR-PAX3, a reciprocal fusion gene of the t(2;13) chromosomal translocation in alveolar rhabdomyosarcomaSplice variants of the forkhead box protein AFX exhibit dominant negative activity and inhibit AFXalpha-mediated tumor cell apoptosis.FOXOs, cancer and regulation of apoptosisChromosomal rearrangement of the PAX-5 locus in lymphoplasmacytic lymphoma with t(9;14)(p13;q32).Preclinical experimental therapeutic approaches in soft tissue sarcoma.Pediatric Rhabdomyosarcoma.Increased levels of forkhead box M1B transcription factor in transgenic mouse hepatocytes prevent age-related proliferation defects in regenerating liver.An engineered PAX3-KRAB transcriptional repressor inhibits the malignant phenotype of alveolar rhabdomyosarcoma cells harboring the endogenous PAX3-FKHR oncogeneAnimal models of soft-tissue sarcoma.Gene fusions involving PAX and FOX family members in alveolar rhabdomyosarcoma.Pax3-FKHR knock-in mice show developmental aberrations but do not develop tumors.The many forks in FOXO's road.Insulin and LiCl synergistically rescue myogenic differentiation of FoxO1 over-expressed myoblastsStrong immunostaining for myogenin in rhabdomyosarcoma is significantly associated with tumors of the alveolar subclass.Childhood rhabdomyosarcoma: recent advances and prospective views.Fusion genes resulting from alternative chromosomal translocations are overexpressed by gene-specific mechanisms in alveolar rhabdomyosarcoma.Coordinated oncogenic transformation and inhibition of host immune responses by the PAX3-FKHR fusion oncoprotein.cDNA microarrays detect activation of a myogenic transcription program by the PAX3-FKHR fusion oncogene.Molecular alterations in pediatric sarcomas: potential targets for immunotherapyClinical relevance of molecular genetics to paediatric sarcomasPigmentation PAX-ways: the role of Pax3 in melanogenesis, melanocyte stem cell maintenance, and diseaseSmall molecule inhibition of PAX3-FOXO1 through AKT activation suppresses malignant phenotypes of alveolar rhabdomyosarcomaHelicase CHD4 is an epigenetic coregulator of PAX3-FOXO1 in alveolar rhabdomyosarcoma.High expression of the PAX3-FKHR oncoprotein is required to promote tumorigenesis of human myoblastsMolecular and cellular biology of rhabdomyosarcoma.Caveolins in rhabdomyosarcomaModeling sarcomagenesis using multipotent mesenchymal stem cells.A call to ARMS: targeting the PAX3-FOXO1 gene in alveolar rhabdomyosarcoma.
P2860
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P2860
The hybrid PAX3-FKHR fusion protein of alveolar rhabdomyosarcoma transforms fibroblasts in culture
description
1996 nî lūn-bûn
@nan
1996 թուականի Սեպտեմբերին հրատարակուած գիտական յօդուած
@hyw
1996 թվականի սեպտեմբերին հրատարակված գիտական հոդված
@hy
1996年の論文
@ja
1996年論文
@yue
1996年論文
@zh-hant
1996年論文
@zh-hk
1996年論文
@zh-mo
1996年論文
@zh-tw
1996年论文
@wuu
name
The hybrid PAX3-FKHR fusion pr ...... nsforms fibroblasts in culture
@ast
The hybrid PAX3-FKHR fusion pr ...... nsforms fibroblasts in culture
@en
The hybrid PAX3-FKHR fusion pr ...... nsforms fibroblasts in culture
@nl
type
label
The hybrid PAX3-FKHR fusion pr ...... nsforms fibroblasts in culture
@ast
The hybrid PAX3-FKHR fusion pr ...... nsforms fibroblasts in culture
@en
The hybrid PAX3-FKHR fusion pr ...... nsforms fibroblasts in culture
@nl
prefLabel
The hybrid PAX3-FKHR fusion pr ...... nsforms fibroblasts in culture
@ast
The hybrid PAX3-FKHR fusion pr ...... nsforms fibroblasts in culture
@en
The hybrid PAX3-FKHR fusion pr ...... nsforms fibroblasts in culture
@nl
P2093
P2860
P356
P1476
The hybrid PAX3-FKHR fusion pr ...... nsforms fibroblasts in culture
@en
P2093
F J Rauscher
S Scheidler
W J Fredericks
P2860
P304
P356
10.1073/PNAS.93.18.9805
P407
P50
P577
1996-09-01T00:00:00Z