Genetic compensation for sarcoglycan loss by integrin alpha7beta1 in muscle
about
Developmental and pathogenic mechanisms of basement membrane assemblyDistinct roles for laminin globular domains in laminin alpha1 chain mediated rescue of murine laminin alpha2 chain deficiencyAbsence of alpha 7 integrin in dystrophin-deficient mice causes a myopathy similar to Duchenne muscular dystrophyCytoplasmic gamma-actin expression in diverse animal models of muscular dystrophyModulation of alpha7-integrin-mediated adhesion and expression by platelet-derived growth factor in vascular smooth muscle cellsThe amphoterin (HMGB1)/receptor for advanced glycation end products (RAGE) pair modulates myoblast proliferation, apoptosis, adhesiveness, migration, and invasiveness. Functional inactivation of RAGE in L6 myoblasts results in tumor formation in vivThe Dystrophin Complex: Structure, Function, and Implications for TherapyLaminin alpha1 chain mediated reduction of laminin alpha2 chain deficient muscular dystrophy involves integrin alpha7beta1 and dystroglycan.Limb-girdle muscular dystrophies: where next after six decades from the first proposal (Review).Restoration of gamma-sarcoglycan localization and mechanical signal transduction are independent in murine skeletal muscle.Gamma-sarcoglycan is required for the response of archvillin to mechanical stimulation in skeletal muscle.Metatranscriptomic Analysis of Pycnopodia helianthoides (Asteroidea) Affected by Sea Star Wasting DiseaseAlpha7beta1 integrin does not alleviate disease in a mouse model of limb girdle muscular dystrophy type 2FSarcoglycanopathies: molecular pathogenesis and therapeutic prospectsβ1D chain increases α7β1 integrin and laminin and protects against sarcolemmal damage in mdx miceDeletion of integrin-linked kinase from skeletal muscles of mice resembles muscular dystrophy due to alpha 7 beta 1-integrin deficiency.Integrin signaling is critical for pathological angiogenesisDystrophin and utrophin expression require sarcospan: loss of α7 integrin exacerbates a newly discovered muscle phenotype in sarcospan-null mice.Increasing alpha 7 beta 1-integrin promotes muscle cell proliferation, adhesion, and resistance to apoptosis without changing gene expression.Laminin-111 restores regenerative capacity in a mouse model for alpha7 integrin congenital myopathyResidual laminin-binding activity and enhanced dystroglycan glycosylation by LARGE in novel model mice to dystroglycanopathy.Thrombospondin expression in myofibers stabilizes muscle membranes.Polymersome delivery of siRNA and antisense oligonucleotides.α6β1 and α7β1 integrins are required in Schwann cells to sort axons.What do mouse models of muscular dystrophy tell us about the DAPC and its components?Transcriptional profile of GTP-mediated differentiation of C2C12 skeletal muscle cells.Deletion of integrin α7 subunit does not aggravate the phenotype of laminin α2 chain-deficient mice.Leaky ryanodine receptors in β-sarcoglycan deficient mice: a potential common defect in muscular dystrophy.Upregulation of paxillin and focal adhesion signaling follows Dystroglycan Complex deletions and promotes a hypertensive state of differentiation.Altered biomechanical properties of carotid arteries in two mouse models of muscular dystrophy.Unraveling the role of membrane proteins Notch, Pvr, and EGFR in altering integrin diffusion and clustering.
P2860
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P2860
Genetic compensation for sarcoglycan loss by integrin alpha7beta1 in muscle
description
2004 nî lūn-bûn
@nan
2004 թուականի Օգոստոսին հրատարակուած գիտական յօդուած
@hyw
2004 թվականի օգոստոսին հրատարակված գիտական հոդված
@hy
2004年の論文
@ja
2004年論文
@yue
2004年論文
@zh-hant
2004年論文
@zh-hk
2004年論文
@zh-mo
2004年論文
@zh-tw
2004年论文
@wuu
name
Genetic compensation for sarcoglycan loss by integrin alpha7beta1 in muscle
@ast
Genetic compensation for sarcoglycan loss by integrin alpha7beta1 in muscle
@en
Genetic compensation for sarcoglycan loss by integrin alpha7beta1 in muscle
@nl
type
label
Genetic compensation for sarcoglycan loss by integrin alpha7beta1 in muscle
@ast
Genetic compensation for sarcoglycan loss by integrin alpha7beta1 in muscle
@en
Genetic compensation for sarcoglycan loss by integrin alpha7beta1 in muscle
@nl
prefLabel
Genetic compensation for sarcoglycan loss by integrin alpha7beta1 in muscle
@ast
Genetic compensation for sarcoglycan loss by integrin alpha7beta1 in muscle
@en
Genetic compensation for sarcoglycan loss by integrin alpha7beta1 in muscle
@nl
P2093
P3181
P356
P1476
Genetic compensation for sarcoglycan loss by integrin alpha7beta1 in muscle
@en
P2093
Andrew A Hack
Elizabeth M McNally
Michael J Allikian
Stephanie Mewborn
P304
P3181
P356
10.1242/JCS.01234
P407
P50
P577
2004-07-13T00:00:00Z