A defect in the mitochondrial complex III, but not complex IV, triggers early ROS-dependent damage in defined brain regions.
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Mitochondrial cytochrome c oxidase deficiencyMitochondrial DNA damage induced autophagy, cell death, and diseasePartial complex I deficiency due to the CNS conditional ablation of Ndufa5 results in a mild chronic encephalopathy but no increase in oxidative damage.Coenzyme q and the respiratory chain: coenzyme q pool and mitochondrial supercomplexesExamination of bioenergetic function in the inner mitochondrial membrane peptidase 2-like (Immp2l) mutant mice.Mitochondrial Diseases Part I: mouse models of OXPHOS deficiencies caused by defects in respiratory complex subunits or assembly factors.Mitochondrial vulnerability and increased susceptibility to nutrient-induced cytotoxicity in fibroblasts from leigh syndrome French canadian patients.The Mitochondrial m-AAA Protease Prevents Demyelination and Hair Greying.A Metabolic Signature of Mitochondrial Dysfunction Revealed through a Monogenic Form of Leigh SyndromeCre recombinase activity is inhibited in vivo but not ex vivo by a mutation in the asymmetric spacer region of the distal loxP site.Mitochondrial function and lifespan of mice with controlled ubiquinone biosynthesisMitochondrial disease: mtDNA and protein segregation mysteries in iPSCsIdentification of chemicals that mimic transcriptional changes associated with autism, brain aging and neurodegeneration.Mutations in CYC1, encoding cytochrome c1 subunit of respiratory chain complex III, cause insulin-responsive hyperglycemia.Sensory cortex limits cortical maps and drives top-down plasticity in thalamocortical circuits.Cytochrome c Oxidase Activity Is a Metabolic Checkpoint that Regulates Cell Fate Decisions During T Cell Activation and Differentiation.MitoTALEN: A General Approach to Reduce Mutant mtDNA Loads and Restore Oxidative Phosphorylation Function in Mitochondrial Diseases.Review: Central nervous system involvement in mitochondrial diseaseCytochrome c oxidase deficiency accelerates mitochondrial apoptosis by activating ceramide synthase 6.Sustained AMPK activation improves muscle function in a mitochondrial myopathy mouse model by promoting muscle fiber regeneration.RETRACTED: Bezafibrate improves mitochondrial function in the CNS of a mouse model of mitochondrial encephalopathy.Deletion of Pim kinases elevates the cellular levels of reactive oxygen species and sensitizes to K-Ras-induced cell killing.Muscle-specific deletion of Prkaa1 enhances skeletal muscle lipid accumulation in mice fed a high-fat diet.Platelet mitochondrial dysfunction and the correlation with human diseases.DARS2 protects against neuroinflammation and apoptotic neuronal loss, but is dispensable for myelin producing cells.The effect of carabrone on mitochondrial respiratory chain complexes in Gaeumannomyces graminis.Mitochondrial retrograde signaling in the nervous system.Mitochondrial DNA damage and reactive oxygen species in neurodegenerative disease.Novel TTC19 mutation in a family with severe psychiatric manifestations and complex III deficiencyPhenotypic variation ofTTC19-deficient mitochondrial complex III deficiency: A case report and literature review
P2860
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P2860
A defect in the mitochondrial complex III, but not complex IV, triggers early ROS-dependent damage in defined brain regions.
description
2012 nî lūn-bûn
@nan
2012 թուականի Օգոստոսին հրատարակուած գիտական յօդուած
@hyw
2012 թվականի օգոստոսին հրատարակված գիտական հոդված
@hy
2012年の論文
@ja
2012年学术文章
@wuu
2012年学术文章
@zh-cn
2012年学术文章
@zh-hans
2012年学术文章
@zh-my
2012年学术文章
@zh-sg
2012年學術文章
@yue
name
A defect in the mitochondrial ...... mage in defined brain regions.
@ast
A defect in the mitochondrial ...... mage in defined brain regions.
@en
type
label
A defect in the mitochondrial ...... mage in defined brain regions.
@ast
A defect in the mitochondrial ...... mage in defined brain regions.
@en
prefLabel
A defect in the mitochondrial ...... mage in defined brain regions.
@ast
A defect in the mitochondrial ...... mage in defined brain regions.
@en
P2093
P2860
P356
P1476
A defect in the mitochondrial ...... amage in defined brain regions
@en
P2093
Carlos T Moraes
Francisca Diaz
Sofia Garcia
P2860
P304
P356
10.1093/HMG/DDS350
P50
P577
2012-08-21T00:00:00Z