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Transmissible Spongiform Encephalopathies Affecting HumansSpontaneous generation of prion infectivity in fatal familial insomnia knockin miceMolecular Pathological Classification of Neurodegenerative Diseases: Turning towards Precision MedicineThe prion protein binds thiamineNeuroimaging biomarkers of neurodegenerative diseases and dementiaA proposal of new diagnostic pathway for fatal familial insomniaAnalyses of the survival time and the influencing factors of chinese patients with prion diseases based on the surveillance data from 2008-2011.Surveillance for Creutzfeldt-Jakob disease in China from 2006 to 2007.Evaluation of the possible transmission of BSE and scrapie to gilthead sea bream (Sparus aurata)Intracerebral distribution of the abnormal isoform of the prion protein in sporadic Creutzfeldt-Jakob disease and fatal insomnia.Midbrain hypometabolism in fatal familial insomnia: a case report and a statistical parametric mapping analysis of a korean family.Transgenic fatal familial insomnia mice indicate prion infectivity-independent mechanisms of pathogenesis and phenotypic expression of disease.Phenotypic variability in familial prion diseases due to the D178N mutation.Selective neuronal vulnerability in human prion diseases. Fatal familial insomnia differs from other types of prion diseases.Mouse-adapted scrapie strains 139A and ME7 overcome species barrier to induce experimental scrapie in hamsters and changed their pathogenic features.Neuroimaging findings in human prion disease.Human prion disease with a G114V mutation and epidemiological studies in a Chinese family: a case series.Lack of TAR-DNA binding protein-43 (TDP-43) pathology in human prion diseases.Small-molecule theranostic probes: a promising future in neurodegenerative diseases.Experimental Models of Inherited PrP Prion Diseases.Sporadic fatal insomnia with spongiform degeneration in the thalamus and widespread PrPSc deposits in the brain.Ultrastructural characteristics (or evaluation) of Creutzfeldt-Jakob disease and other human transmissible spongiform encephalopathies or prion diseases.Severe brain atrophy in a case of thalamic variant of sporadic CJD with plaque-like PrP deposition.The diversities of PrP(Sc) distributions and pathologic changes in various brain regions from a Chinese patient with G114V genetic CJD.Identification of new molecular alterations in fatal familial insomnia.Ultrastructural pathology of prion diseases revisited: brain biopsy studies.Fatal familial insomnia with an unusual prion protein deposition pattern: an autopsy report with an experimental transmission study.
P2860
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P2860
description
1999 nî lūn-bûn
@nan
1999 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
1999 թվականի հունվարին հրատարակված գիտական հոդված
@hy
1999年の論文
@ja
1999年学术文章
@wuu
1999年学术文章
@zh-cn
1999年学术文章
@zh-hans
1999年学术文章
@zh-my
1999年学术文章
@zh-sg
1999年學術文章
@yue
name
Fatal familial insomnia: a new Austrian family.
@ast
Fatal familial insomnia: a new Austrian family.
@en
type
label
Fatal familial insomnia: a new Austrian family.
@ast
Fatal familial insomnia: a new Austrian family.
@en
prefLabel
Fatal familial insomnia: a new Austrian family.
@ast
Fatal familial insomnia: a new Austrian family.
@en
P2093
P356
P1433
P1476
Fatal familial insomnia: a new Austrian family.
@en
P2093
Collinge J
Hainfellner JA
Jellinger K
Kleinert R
Kretzschmar HA
P356
10.1093/BRAIN/122.1.5
P407
P478
122 ( Pt 1)
P577
1999-01-01T00:00:00Z