Involvement of mitochondrial complex II defects in neuronal death produced by N-terminus fragment of mutated huntingtin - Wikidata - awgldk - TriplyDB

Involvement of mitochondrial complex II defects in neuronal death produced by N-terminus fragment of mutated huntingtin

Involvement of mitochondrial complex II defects in neuronal death produced by N-terminus fragment of mutated huntingtin

http://www.wikidata.org/entity/Q34483577

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New insights into the role of mitochondria in aging: mitochondrial dynamics and more Old Things New View: Ascorbic Acid Protects the Brain in Neurodegenerative Disorders Electron Transport Disturbances and Neurodegeneration: From Albert Szent-Györgyi's Concept (Szeged) till Novel Approaches to Boost Mitochondrial Bioenergetics Iron dysregulation in Huntington's disease Physiological consequences of complex II inhibition for aging, disease, and the mKATP channel Possible involvement of self-defense mechanisms in the preferential vulnerability of the striatum in Huntington's disease The chicken or the egg: mitochondrial dysfunction as a cause or consequence of toxicity in Huntington's disease Mitochondrial fragmentation in neurodegeneration Shaping the role of mitochondria in the pathogenesis of Huntington's disease Role of oxidative DNA damage in mitochondrial dysfunction and Huntington's disease pathogenesis N-Acetylcysteine improves mitochondrial function and ameliorates behavioral deficits in the R6/1 mouse model of Huntington's disease Enhanced neuronal glucose transporter expression reveals metabolic choice in a HD Drosophila model Homeostatic adaptations in brain energy metabolism in mouse models of Huntington disease Metabolism in HD: still a relevant mechanism?N-terminal mutant huntingtin associates with mitochondria and impairs mitochondrial trafficking.Dysregulated brain creatine kinase is associated with hearing impairment in mouse models of Huntington disease Knockdown of cytosolic glutaredoxin 1 leads to loss of mitochondrial membrane potential: implication in neurodegenerative diseases Guinea pig horizontal cells express GABA, the GABA-synthesizing enzyme GAD 65, and the GABA vesicular transporter.Coexpression within Integrated Mitochondrial Pathways Reveals Different Networks in Normal and Chemically Treated Transcriptomes.D-β-hydroxybutyrate is protective in mouse models of Huntington's disease.Impaired mitochondrial respiration and protein nitration in the rat hippocampus after acute inhalation of combustion smoke.Therapeutic approaches to preventing cell death in Huntington disease Delayed Onset and Reduced Cognitive Deficits through Pre-Conditioning with 3-Nitropropionic Acid is Dependent on Sex and CAG Repeat Length in the R6/2 Mouse Model of Huntington's Disease.Dysfunctional mitochondrial respiration in the striatum of the Huntington's disease transgenic R6/2 mouse model.Forebrain striatal-specific expression of mutant huntingtin protein in vivo induces cell-autonomous age-dependent alterations in sensitivity to excitotoxicity and mitochondrial function.Huntington's Disease and Striatal Signaling.IRS2 increases mitochondrial dysfunction and oxidative stress in a mouse model of Huntington disease Abnormalities in the tricarboxylic Acid cycle in Huntington disease and in a Huntington disease mouse model.Mitochondrial DNA damage is a hallmark of chemically induced and the R6/2 transgenic model of Huntington's disease Cardiac dysfunction in the R6/2 mouse model of Huntington's disease Mutations in cytochrome c oxidase subunit VIa cause neurodegeneration and motor dysfunction in Drosophila Calcium Handling by Endoplasmic Reticulum and Mitochondria in a Cell Model of Huntington's Disease.Novel Metabolic Abnormalities in the Tricarboxylic Acid Cycle in Peripheral Cells From Huntington's Disease Patients Dysregulation of mitochondrial calcium signaling and superoxide flashes cause mitochondrial genomic DNA damage in Huntington disease.CYP46A1, the rate-limiting enzyme for cholesterol degradation, is neuroprotective in Huntington's disease.Secrets of the lac operon. Glucose hysteresis as a mechanism in dietary restriction, aging and disease.Translational research in Huntington's disease: opening up for disease modifying treatment Isolated cytochrome c oxidase deficiency in G93A SOD1 mice overexpressing CCS protein Mitochondria in neurodegeneration.Transcriptional signatures in Huntington's disease.

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Involvement of mitochondrial complex II defects in neuronal death produced by N-terminus fragment of mutated huntingtin

http://www.wikidata.org/entity/Q34483577

description

2006 nî lūn-bûn

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2006 թուականի Փետրուարին հրատարակուած գիտական յօդուած

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2006 թվականի փետրվարին հրատարակված գիտական հոդված

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2006年の論文

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2006年論文

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2006年論文

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2006年論文

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2006年論文

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2006年論文

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2006年论文

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Involvement of mitochondrial c ...... fragment of mutated huntingtin

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Involvement of mitochondrial c ...... fragment of mutated huntingtin

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Involvement of mitochondrial c ...... fragment of mutated huntingtin

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Involvement of mitochondrial c ...... fragment of mutated huntingtin

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Involvement of mitochondrial c ...... fragment of mutated huntingtin

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Involvement of mitochondrial c ...... fragment of mutated huntingtin

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Involvement of mitochondrial c ...... fragment of mutated huntingtin

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Involvement of mitochondrial c ...... fragment of mutated huntingtin

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Involvement of mitochondrial c ...... fragment of mutated huntingtin

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MBC.E05-07-0607

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Molecular Biology of the Cell

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Involvement of mitochondrial c ...... fragment of mutated huntingtin

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Jean-Marc Elalouf

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Marie-Claude Gaillard

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Nathalie Lefort

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Noelle Dufour

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Philippe Hantraye

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Yaël Trioulier

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P2860

Mutation of a nuclear succinate dehydrogenase gene results in mitochondrial respiratory chain deficiency

PUMA couples the nuclear and cytoplasmic proapoptotic function of p53

Tight control of gene expression in mammalian cells by tetracycline-responsive promoters

Translational regulation of mammalian and Drosophila citric acid cycle enzymes via iron-responsive elements

Single-Step Method of RNA Isolation by Acid Guanidinium Thiocyanate–Phenol–Chloroform Extraction

A novel gene containing a trinucleotide repeat that is expanded and unstable on Huntington's disease chromosomes.

Huntingtin interacts with REST/NRSF to modulate the transcription of NRSE-controlled neuronal genes

Huntingtin and its role in neuronal degeneration

The R22X mutation of the SDHD gene in hereditary paraganglioma abolishes the enzymatic activity of complex II in the mitochondrial respiratory chain and activates the hypoxia pathway

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1652-1663

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scholarly article

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10.1091/MBC.E05-07-0607

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4

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17

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Emmanuel Brouillet

Alexandra Benchoua

Frédéric Saudou

Etienne C. Hirsch

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2006-02-01T00:00:00Z

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7320899

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16452635

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1415305

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