Mislocalization and degradation of human P23H-rhodopsin-GFP in a knockin mouse model of retinitis pigmentosa
about
Abrupt onset of mutations in a developmentally regulated gene during terminal differentiation of post-mitotic photoreceptor neurons in mice.Photoactivation-induced instability of rhodopsin mutants T4K and T17M in rod outer segments underlies retinal degeneration in X. laevis transgenic models of retinitis pigmentosaRhodopsin gene expression determines rod outer segment size and rod cell resistance to a dominant-negative neurodegeneration mutantMfsd2a Is a Transporter for the Essential ω-3 Fatty Acid Docosahexaenoic Acid (DHA) in Eye and Is Important for Photoreceptor Cell DevelopmentDetermining Membrane Protein Topology Using Fluorescence Protease Protection (FPP).Misfolded opsin mutants display elevated β-sheet structure.Molecular studies of phenotype variation in canine RPGR-XLPRA1.Two-Step Reactivation of Dormant Cones in Retinitis PigmentosaThe severe autosomal dominant retinitis pigmentosa rhodopsin mutant Ter349Glu mislocalizes and induces rapid rod cell death.P23H opsin knock-in mice reveal a novel step in retinal rod disc morphogenesis.Fluorescence spectroscopy of rhodopsins: insights and approaches.Progression of Pro23His Retinopathy in a Miniature Swine Model of Retinitis Pigmentosa.Translational and posttranslational regulation of XIAP by eIF2α and ATF4 promotes ER stress-induced cell death during the unfolded protein response.Fluorescent knock-in mice to decipher the physiopathological role of G protein-coupled receptors.Molecular basis for photoreceptor outer segment architecture.A Pro23His mutation alters prenatal rod photoreceptor morphology in a transgenic swine model of retinitis pigmentosa.Prenatal Exposure to Curcumin Protects Rod Photoreceptors in a Transgenic Pro23His Swine Model of Retinitis Pigmentosa.Protective effect of clusterin on rod photoreceptor in rat model of retinitis pigmentosaRestoration of Cone Photoreceptor Function in Retinitis PigmentosaWild-type opsin does not aggregate with a misfolded opsin mutant.Assessing the correlation between mutant rhodopsin stability and the severity of retinitis pigmentosaEndoplasmic reticulum stress in vertebrate mutant rhodopsin models of retinal degeneration.Can fly photoreceptors lead to treatments for rho ((P23H)) -linked retinitis pigmentosa?The molecular and cellular basis of rhodopsin retinitis pigmentosa reveals potential strategies for therapy.Phenotypic characterization of P23H and S334ter rhodopsin transgenic rat models of inherited retinal degeneration.Retinitis pigmentosa: impact of different Pde6a point mutations on the disease phenotype.Dominant and recessive mutations in rhodopsin activate different cell death pathways.Tissue inhibitor of metalloproteinases 1 enhances rod survival in the rd1 mouse retina.Targeted disruption of the endogenous zebrafish locus as models of rapid rod photoreceptor degeneration
P2860
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P2860
Mislocalization and degradation of human P23H-rhodopsin-GFP in a knockin mouse model of retinitis pigmentosa
description
2011 nî lūn-bûn
@nan
2011年の論文
@ja
2011年論文
@yue
2011年論文
@zh-hant
2011年論文
@zh-hk
2011年論文
@zh-mo
2011年論文
@zh-tw
2011年论文
@wuu
2011年论文
@zh
2011年论文
@zh-cn
name
Mislocalization and degradatio ...... model of retinitis pigmentosa
@ast
Mislocalization and degradatio ...... model of retinitis pigmentosa
@en
type
label
Mislocalization and degradatio ...... model of retinitis pigmentosa
@ast
Mislocalization and degradatio ...... model of retinitis pigmentosa
@en
prefLabel
Mislocalization and degradatio ...... model of retinitis pigmentosa
@ast
Mislocalization and degradatio ...... model of retinitis pigmentosa
@en
P2093
P2860
P356
P1476
Mislocalization and degradatio ...... model of retinitis pigmentosa
@en
P2093
Brandee A Price
David L Simons
Ivette M Sandoval
John H Wilson
Samuel M Wu
P2860
P304
P356
10.1167/IOVS.11-8654
P407
P577
2011-12-28T00:00:00Z