about
The hyperimmunoglobulin E syndrome--clinical manifestation diversity in primary immune deficiencyMendelian genetics of human susceptibility to fungal infectionCancers Related to Immunodeficiencies: Update and PerspectivesSTAT3 single-nucleotide polymorphisms and STAT3 mutations associated with hyper-IgE syndrome are not responsible for increased serum IgE serum levels in asthma families.Staphylococcus aureus - antimicrobial resistance and the immunocompromised child.B cell-intrinsic signaling through IL-21 receptor and STAT3 is required for establishing long-lived antibody responses in humans.Large deletions and point mutations involving the dedicator of cytokinesis 8 (DOCK8) in the autosomal-recessive form of hyper-IgE syndrome.Hyperimmunoglobulin E syndrome: Genetics, immunopathogenesis, clinical findings, and treatment modalitiesRapid molecular analysis of the STAT3 gene in Job syndrome of hyper-IgE and recurrent infectious diseasesMutations in STAT3 and diagnostic guidelines for hyper-IgE syndromeAcupuncture for symptom management in patients with hyper-IgE (Job's) syndrome.Defective IL-10 signaling in hyper-IgE syndrome results in impaired generation of tolerogenic dendritic cells and induced regulatory T cells.Primary immunodeficiencies: a field in its infancy.Adaptive immunity to fungi.A Case of Hyper Immunoglobulin-E Syndrome Associated with Scrotal Tongue and Intraoral Hyperpigmentation.Profile of the patients who present to immunology outpatient clinics because of frequent infections.Sequential class switching is required for the generation of high affinity IgE antibodies.Hyper Ig E syndrome (Job syndrome, HIES) - radiological images of pulmonary complications on the basis of three casesLaboratory evaluation of primary immunodeficienciesEvaluation and differential diagnosis of marked, persistent eosinophilia.Signal transducer and activator of transcription 3 mutation with invasive eosinophilic diseaseThe influence of commensal bacteria-derived signals on basophil-associated allergic inflammation.Immunity to microbes: lessons from primary immunodeficiencies.Deficiency of Th17 cells in hyper IgE syndrome due to mutations in STAT3Clearance of Staphylococcus aureus nasal carriage is T cell dependent and mediated through interleukin-17A expression and neutrophil influxAutosomal dominant STAT3 deficiency and hyper-IgE syndrome: molecular, cellular, and clinical features from a French national survey129/SvJ mice have mutated CD23 and hyper IgEFalse negative PCR despite high levels of JC virus DNA in spinal fluid: Implications for diagnostic testingSignal transducer and activator of transcription 3 (STAT3) mutations underlying autosomal dominant hyper-IgE syndrome impair human CD8(+) T-cell memory formation and function.Molecular explanation for the contradiction between systemic Th17 defect and localized bacterial infection in hyper-IgE syndromeDefects in Jak-STAT-mediated cytokine signals cause hyper-IgE syndrome: lessons from a primary immunodeficiency.Cytokine-Mediated Regulation of Plasma Cell Generation: IL-21 Takes Center Stage.Factors associated with bronchiectasis in patients with moderate-severe chronic obstructive pulmonary disease.A review on the vascular features of the hyperimmunoglobulin E syndrome.Diffuse large B cell lymphoma in hyper-IgE syndrome due to STAT3 mutation.Molecular mechanisms of the immunological abnormalities in hyper-IgE syndrome.TH17 deficiency in human disease.Hematopoietic stem cell transplantation from unrelated donors in children with DOCK8 deficiency.STAT3 mutations correlated with hyper-IgE syndrome lead to blockage of IL-6/STAT3 signalling pathway.Variation in genes of β-glucan recognition pathway and susceptibility to opportunistic infections in HIV-positive patients.
P2860
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P2860
description
2005 nî lūn-bûn
@nan
2005年の論文
@ja
2005年学术文章
@wuu
2005年学术文章
@zh-cn
2005年学术文章
@zh-hans
2005年学术文章
@zh-my
2005年学术文章
@zh-sg
2005年學術文章
@yue
2005年學術文章
@zh
2005年學術文章
@zh-hant
name
Hyper-IgE syndromes.
@ast
Hyper-IgE syndromes.
@en
type
label
Hyper-IgE syndromes.
@ast
Hyper-IgE syndromes.
@en
prefLabel
Hyper-IgE syndromes.
@ast
Hyper-IgE syndromes.
@en
P2093
P2860
P1476
Hyper-IgE syndromes.
@en
P2093
Bodo Grimbacher
Jennifer M Puck
Steven M Holland
P2860
P304
P356
10.1111/J.0105-2896.2005.00228.X
P577
2005-02-01T00:00:00Z