Role of calnexin in the ER quality control and productive folding of CFTR; differential effect of calnexin knockout on wild-type and DeltaF508 CFTR.

Role of calnexin in the ER quality control and productive folding of CFTR; differential effect of calnexin knockout on wild-type and DeltaF508 CFTR.

Item
http://www.wikidata.org/entity/Q39985271
Molecular Chaperones as Targets to Circumvent the CFTR Defect in Cystic FibrosisCFTR Modulators: Shedding Light on Precision Medicine for Cystic FibrosisCo- and Post-Translational Protein Folding in the EREmergent properties of proteostasis in managing cystic fibrosis.Effects of cellular, chemical, and pharmacological chaperones on the rescue of a trafficking-defective mutant of the ATP-binding cassette transporter proteins ABCB1/ABCB4.Assembly and misassembly of cystic fibrosis transmembrane conductance regulator: folding defects caused by deletion of F508 occur before and after the calnexin-dependent association of membrane spanning domain (MSD) 1 and MSD2N-glycans are direct determinants of CFTR folding and stability in secretory and endocytic membrane traffic.Role of N-linked oligosaccharides in the biosynthetic processing of the cystic fibrosis membrane conductance regulator.Trafficking and function of the cystic fibrosis transmembrane conductance regulator: a complex network of posttranslational modifications.Cell surface rescue of kidney anion exchanger 1 mutants by disruption of chaperone interactions.Calnexin improves the folding efficiency of mutant rhodopsin in the presence of pharmacological chaperone 11-cis-retinal.The Cacna1h mutation in the GAERS model of absence epilepsy enhances T-type Ca2+ currents by altering calnexin-dependent trafficking of Cav3.2 channels.Loss of specific chaperones involved in membrane glycoprotein biosynthesis during the maturation of human erythroid progenitor cells.Airway delivery of low-dose miglustat normalizes nasal potential difference in F508del cystic fibrosis mice.Peripheral Protein Quality Control as a Novel Drug Target for CFTR Stabilizer
P2860

Role of calnexin in the ER quality control and productive folding of CFTR; differential effect of calnexin knockout on wild-type and DeltaF508 CFTR.

Item
http://www.wikidata.org/entity/Q39985271
description
2008 nî lūn-bûn
@nan
2008年の論文
@ja
2008年学术文章
@wuu
2008年学术文章
@zh-cn
2008年学术文章
@zh-hans
2008年学术文章
@zh-my
2008年学术文章
@zh-sg
2008年學術文章
@yue
2008年學術文章
@zh
2008年學術文章
@zh-hant
name
Role of calnexin in the ER qua ...... wild-type and DeltaF508 CFTR.
@en
Role of calnexin in the ER qua ...... wild-type and DeltaF508 CFTR.
@nl
type
label
Role of calnexin in the ER qua ...... wild-type and DeltaF508 CFTR.
@en
Role of calnexin in the ER qua ...... wild-type and DeltaF508 CFTR.
@nl
prefLabel
Role of calnexin in the ER qua ...... wild-type and DeltaF508 CFTR.
@en
Role of calnexin in the ER qua ...... wild-type and DeltaF508 CFTR.
@nl
P1433
P1476
P2093
P304
P31
P356
P433
P478
P50
P577
P5875
P698
P921
P356
P1433
P1476
Role of calnexin in the ER qua ...... wild-type and DeltaF508 CFTR.
@en
P2093
P304
P31
P356
10.1016/J.BBAMCR.2008.04.002
P433
P478
P50
P577
P5875
P698
P921