Severe ultrastructural mitochondrial changes in lymphoblasts homozygous for Huntington disease mutation.
about
New insights into the role of mitochondria in aging: mitochondrial dynamics and moreOxidative stress, mitochondrial dysfunction, and agingTranscriptional dysregulation in Huntington's disease: a failure of adaptive transcriptional homeostasisThe chicken or the egg: mitochondrial dysfunction as a cause or consequence of toxicity in Huntington's diseaseShaping the role of mitochondria in the pathogenesis of Huntington's diseaseRole of oxidative DNA damage in mitochondrial dysfunction and Huntington's disease pathogenesisFormation of polyglutamine inclusions in a wide range of non-CNS tissues in the HdhQ150 knock-in mouse model of Huntington's disease.No evidence of impaired gastric emptying in early Huntington's Disease.Increase of angiotensin II type 1 receptor auto-antibodies in Huntington's disease.Cardiac dysfunction in the R6/2 mouse model of Huntington's diseaseCalcium Handling by Endoplasmic Reticulum and Mitochondria in a Cell Model of Huntington's Disease.Impairing the mitochondrial fission and fusion balance: a new mechanism of neurodegeneration.The mitochondrial antioxidants MitoE(2) and MitoQ(10) increase mitochondrial Ca(2+) load upon cell stimulation by inhibiting Ca(2+) efflux from the organelleMutant huntingtin and mitochondrial dysfunction.Mitochondrial approaches for neuroprotectionChipping away at diagnostics for neurodegenerative diseasesOxidative metabolism and Ca2+ handling in isolated brain mitochondria and striatal neurons from R6/2 mice, a model of Huntington's disease.The interrelationship between mitochondrial dysfunction and transcriptional dysregulation in Huntington disease.Molecular mechanisms and potential therapeutical targets in Huntington's disease.Energy dysfunction in Huntington's disease: insights from PGC-1α, AMPK, and CKB.An in vitro perspective on the molecular mechanisms underlying mutant huntingtin protein toxicityThe role of the immune system in Huntington's disease.Mutant Huntingtin induces activation of the Bcl-2/adenovirus E1B 19-kDa interacting protein (BNip3)Metabolic profiling of presymptomatic Huntington's disease sheep reveals novel biomarkers.A study of molecular changes relating to energy metabolism and cellular stress in people with Huntington's disease: looking for biomarkers.Increased apoptosis, Huntingtin inclusions and altered differentiation in muscle cell cultures from Huntington's disease subjects.Genotype-, aging-dependent abnormal caspase activity in Huntington disease blood cells.Effect of a mitochondria-targeted vitamin E derivative on mitochondrial alteration and systemic oxidative stress in mice.Identification of differentially expressed genes and regulatory relationships in Huntington's disease by bioinformatics analysis.Increased nuclear DNA damage precedes mitochondrial dysfunction in peripheral blood mononuclear cells from Huntington's disease patients.Stratifying Heterogeneous Dimension of Neurodegenerative Diseases: Intervention for Stipulating Epigenetic Factors to Combat Oxidative Stress in Human Brain
P2860
Q24600600-3A074F3E-31D0-44A8-A450-455F42E04728Q24635310-AFC5E66F-5FC0-40A1-BD27-BFD3041E3D38Q27026549-13B85EED-A7EE-4AEE-A615-2AB0C8421147Q28072937-D49E0213-0827-4D95-9B15-3FBA0E943126Q28384036-8987F8D6-9283-4914-AD1C-EC79B632F49FQ28386202-19C7F9EF-06C8-486A-BDD4-B8AD4AA8FAB1Q33517121-7239FF80-3EF2-4470-8727-D3E69D7A8CB7Q34087126-7BE468A9-ADE1-4530-8326-13FE90B18841Q34581918-AD44B2C8-3A07-4607-B266-BD57CE266A82Q35745626-460D9425-5494-4CBF-8952-6519C66294CBQ35906784-32816EA0-4C3E-420C-81DC-B5308F6AD158Q37019754-5A167C0D-5F91-46E4-A511-662437CB470BQ37177530-E55B8FCB-8173-4C1B-B9BA-E8BEB1799F6CQ37308357-9CE2A1B4-B2E2-4B58-83B4-4A303B6FD291Q37348590-677AD280-E7CC-47A2-AA67-84C478A19F00Q37366183-223B6F1B-4F85-446E-90B2-3336D0DD019BQ37530288-CC8E0892-8C52-4B03-8DEF-8CC3B5A7FC0BQ37765841-75F1E5B0-186D-480F-B220-EFE7B989976BQ37776087-9A38600F-8CF8-48D9-AA4B-A234C4F30CB1Q38013005-F0298785-7737-452C-BFB8-AE03FCF608A9Q38038981-35014E7D-5F9C-445C-ADCC-4BE76FEF8B8FQ38129870-269E3651-F860-4477-96F0-1799D306F9ADQ39757740-AF557F96-776E-48D7-B9FA-B58C99871B69Q42320470-8DD5BF19-C99B-477D-B889-E9317C9E564EQ45290293-92CD9B0E-D0E6-4BA0-BF68-87CAF23663FEQ45301339-F5C2F576-F5B0-435E-A7B7-E0BF1E4FD0EEQ45302615-249BCCCA-64E8-458F-A1F5-C5B487B42403Q45977766-0F0AAF0D-161D-4141-A280-070CAFD06BD1Q50067763-5A6291B4-5090-45A0-A2FC-B59D60AE0856Q55516044-D5CA64E3-EDE9-4CD2-AC6A-AFBB584DB1FFQ58051863-A526964F-199F-4F13-BA4E-AB6C875EB3DD
P2860
Severe ultrastructural mitochondrial changes in lymphoblasts homozygous for Huntington disease mutation.
description
2005 nî lūn-bûn
@nan
2005年の論文
@ja
2005年論文
@yue
2005年論文
@zh-hant
2005年論文
@zh-hk
2005年論文
@zh-mo
2005年論文
@zh-tw
2005年论文
@wuu
2005年论文
@zh
2005年论文
@zh-cn
name
Severe ultrastructural mitocho ...... r Huntington disease mutation.
@en
type
label
Severe ultrastructural mitocho ...... r Huntington disease mutation.
@en
prefLabel
Severe ultrastructural mitocho ...... r Huntington disease mutation.
@en
P2093
P50
P1476
Severe ultrastructural mitocho ...... r Huntington disease mutation.
@en
P2093
Alessandra Baracca
Alessandra Falleni
Gianluca Sgarbi
Giuliana Cislaghi
Giuseppe Ragona
Leslie M Thompson
Matteo A Russo
P304
P356
10.1016/J.MAD.2005.09.010
P50
P577
2005-11-09T00:00:00Z