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Dystrophins and dystrobrevins.A new twist to coiled coilClinical features of patients with dystrophinopathy sharing the 45-55 exon deletion of DMD geneThe Crystal Structures of Dystrophin and Utrophin Spectrin Repeats: Implications for Domain BoundariesCloning and expression of full length mouse utrophin: the differential association of utrophin and dystrophin with AChR clustersDisruption of the utrophin-actin interaction by monoclonal antibodies and prediction of an actin-binding surface of utrophin.The dystrotelin, dystrophin and dystrobrevin superfamily: new paralogues and old isoforms.The polyproline site in hinge 2 influences the functional capacity of truncated dystrophins.Plasma membrane cytoskeleton of muscle: a fine structural analysis.Sarcolemmal nNOS anchoring reveals a qualitative difference between dystrophin and utrophin.Dystrophins, utrophins, and associated scaffolding complexes: role in mammalian brain and implications for therapeutic strategies.Computational study of the human dystrophin repeats: interaction properties and molecular dynamics.Conservation of components of the dystrophin complex in Drosophila.Missense mutations in dystrophin that trigger muscular dystrophy decrease protein stability and lead to cross-beta aggregates.Spectrin-like repeats 11-15 of human dystrophin show adaptations to a lipidic environment.In vitro stability of therapeutically relevant, internally truncated dystrophins.Multiple pathogenetic mechanisms in X linked dilated cardiomyopathy.Effect of adopting a new histological grading system of acute rejection after heart transplantation.A new model for the interaction of dystrophin with F-actin.Functional characterization of orbicularis oculi and extraocular musclesAssessment of the structural and functional impact of in-frame mutations of the DMD gene, using the tools included in the eDystrophin online databaseRegulation of actin cytoskeleton dynamics in cells.Utrophin lacks the rod domain actin binding activity of dystrophin.Dystrophin and Spectrin, Two Highly Dissimilar Sisters of the Same Family.ABC of multifaceted dystrophin glycoprotein complex (DGC).Hybrid spectrin type repeats produced by exon-skipping in dystrophin.Utrophin: a structural and functional comparison to dystrophin.Novel mutation in spectrin-like repeat 1 of dystrophin central domain causes protein misfolding and mild Becker muscular dystrophy.Thermodynamic stability, unfolding kinetics, and aggregation of the N-terminal actin-binding domains of utrophin and dystrophin.Stability of dystrophin STR fragments in relation to junction helicity.Structural organization of the nine spectrin repeats of Kalirin.Stability of the dystrophin rod domain fold: evidence for nested repeating units.A Two-amino Acid Mutation Encountered in Duchenne Muscular Dystrophy Decreases Stability of the Rod Domain 23 (R23) Spectrin-like Repeat of Dystrophin.The artificial zinc finger coding gene 'Jazz' binds the utrophin promoter and activates transcription.Identification of spectrin-like repeats required for high affinity utrophin-actin interaction.The molecular cross talk of the dystrophin-glycoprotein complex.Co-localization of dystrophin and beta-dystroglycan demonstrated in en face view by double immunogold labeling of freeze-fractured skeletal muscle.Multiple Species Comparison of Cardiac Troponin T and Dystrophin: Unravelling the DNA behind Dilated Cardiomyopathy.Site-directed mutagenesis of either the highly conserved Trp-22 or the moderately conserved Trp-95 to a large, hydrophobic residue reduces the thermodynamic stability of a spectrin repeating unit.Laminins in Epithelial Cell Polarization: Old Questions in Search of New Answers.
P2860
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P2860
description
1995 nî lūn-bûn
@nan
1995年の論文
@ja
1995年論文
@yue
1995年論文
@zh-hant
1995年論文
@zh-hk
1995年論文
@zh-mo
1995年論文
@zh-tw
1995年论文
@wuu
1995年论文
@zh
1995年论文
@zh-cn
name
Dystrophin and utrophin: the missing links!
@en
type
label
Dystrophin and utrophin: the missing links!
@en
prefLabel
Dystrophin and utrophin: the missing links!
@en
P2093
P2860
P1433
P1476
Dystrophin and utrophin: the missing links!
@en
P2093
Kendrick-Jones J
P2860
P356
10.1016/0014-5793(95)00398-S
P407
P577
1995-08-01T00:00:00Z