Osteoblast Malfunction Caused by Cell Stress Response to Procollagen Misfolding in α2(I)-G610C Mouse Model of Osteogenesis Imperfecta.
about
Mapping the Effect of Gly Mutations in Collagen on α2β1 Integrin Binding.Makings of a brittle bone: Unexpected lessons from a low protein diet study of a mouse OI model.The chaperone activity of 4PBA ameliorates the skeletal phenotype of Chihuahua, a zebrafish model for dominant osteogenesis imperfecta.Acidic pH environment induces autophagy in osteoblasts.Adapting Secretory Proteostasis and Function Through the Unfolded Protein Response.4-PBA ameliorates cellular homeostasis in fibroblasts from osteogenesis imperfecta patients by enhancing autophagy and stimulating protein secretion.Insight into the Pathology of a COL1A1 Signal Peptide Heterozygous Mutation Leading to Severe Osteogenesis Imperfecta.Genetic causes and mechanisms of Osteogenesis Imperfecta.Inhibiting the integrated stress response pathway prevents aberrant chondrocyte differentiation thereby alleviating chondrodysplasiaNoncanonical autophagy at ER exit sites regulates procollagen turnoverChaperonin 60 sustains osteoblast autophagy and counteracts glucocorticoid aggravation of osteoporosis by chaperoning RPTOR
P2860
Q37227653-EB473A20-E5FB-47D0-8461-E1AA12E914A8Q37334366-7FAEA838-98A5-44E9-B04E-D2D5DC7E534DQ38802051-887612EA-5B82-4CBF-A68E-3F00FBBB35B3Q41912980-C1608FE5-F5FC-45AF-8D77-20187CAF3870Q47774233-4C04ACFB-56ED-40EC-8EC5-80E3A8F4B5E2Q50060612-F5E41DDA-DABA-41D6-9A9E-FF8529AF6209Q50172577-920ADAEE-88BA-4C3F-B50B-E6A043CB3F41Q52679260-071E3E92-9CFC-4784-A0F7-180650A8FC5EQ56533422-D6AC2B40-F707-4A21-8A0C-BD515C74F8F9Q57031513-2E25E8C2-66F5-472C-ADF7-CD26CDAB190CQ58734395-7FECF615-324E-4F0D-BBBB-C262090C0768
P2860
Osteoblast Malfunction Caused by Cell Stress Response to Procollagen Misfolding in α2(I)-G610C Mouse Model of Osteogenesis Imperfecta.
description
2016 nî lūn-bûn
@nan
2016年の論文
@ja
2016年論文
@yue
2016年論文
@zh-hant
2016年論文
@zh-hk
2016年論文
@zh-mo
2016年論文
@zh-tw
2016年论文
@wuu
2016年论文
@zh
2016年论文
@zh-cn
name
Osteoblast Malfunction Caused ...... el of Osteogenesis Imperfecta.
@en
type
label
Osteoblast Malfunction Caused ...... el of Osteogenesis Imperfecta.
@en
prefLabel
Osteoblast Malfunction Caused ...... el of Osteogenesis Imperfecta.
@en
P2093
P2860
P356
P1476
Osteoblast Malfunction Caused ...... del of Osteogenesis Imperfecta
@en
P2093
Anna M Roberts-Pilgrim
Arin K Oestreich
Edward L Mertz
Elena Makareeva
Lynn S Mirigian
Shakib Omari
P2860
P304
P356
10.1002/JBMR.2824
P577
2016-04-13T00:00:00Z