Postulated role of interdomain interaction between regions 1 and 2 within type 1 ryanodine receptor in the pathogenesis of porcine malignant hyperthermia.
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Divergent Activity Profiles of Type 1 Ryanodine Receptor Channels Carrying Malignant Hyperthermia and Central Core Disease Mutations in the Amino-Terminal RegionLocalization of an NH(2)-terminal disease-causing mutation hot spot to the "clamp" region in the three-dimensional structure of the cardiac ryanodine receptor.Muscle weakness in Ryr1I4895T/WT knock-in mice as a result of reduced ryanodine receptor Ca2+ ion permeation and release from the sarcoplasmic reticulum.Malignant hyperthermia: a pharmacogenetic disorder.Effects of conformational peptide probe DP4 on bidirectional signaling between DHPR and RyR1 calcium channels in voltage-clamped skeletal muscle fibers.Gene dose influences cellular and calcium channel dysregulation in heterozygous and homozygous T4826I-RYR1 malignant hyperthermia-susceptible muscle.Enhanced excitation-coupled calcium entry in myotubes expressing malignant hyperthermia mutation R163C is attenuated by dantrolene.Calcium-induced calcium release in skeletal muscle.Structural and functional interactions within ryanodine receptor.Role of amino-terminal half of the S4-S5 linker in type 1 ryanodine receptor (RyR1) channel gating.Reduced threshold for luminal Ca2+ activation of RyR1 underlies a causal mechanism of porcine malignant hyperthermia.Functional analysis of RYR1 variants linked to malignant hyperthermia.
P2860
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P2860
Postulated role of interdomain interaction between regions 1 and 2 within type 1 ryanodine receptor in the pathogenesis of porcine malignant hyperthermia.
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2007 nî lūn-bûn
@nan
2007年の論文
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2007年論文
@yue
2007年論文
@zh-hant
2007年論文
@zh-hk
2007年論文
@zh-mo
2007年論文
@zh-tw
2007年论文
@wuu
2007年论文
@zh
2007年论文
@zh-cn
name
Postulated role of interdomain ...... orcine malignant hyperthermia.
@en
type
label
Postulated role of interdomain ...... orcine malignant hyperthermia.
@en
prefLabel
Postulated role of interdomain ...... orcine malignant hyperthermia.
@en
P2093
P2860
P356
P1433
P1476
Postulated role of interdomain ...... orcine malignant hyperthermia.
@en
P2093
Hiroshi Hara
Kikuo Wakebe
Noriaki Ikemoto
Takashi Murayama
Toshiharu Oba
Yasuo Ogawa
P2860
P304
P356
10.1042/BJ20061040
P407
P577
2007-03-01T00:00:00Z