Intracellular storage and regulated secretion of von Willebrand factor in quantitative von Willebrand disease
about
Weibel-Palade bodies: a window to von Willebrand disease.Chemical chaperones improve protein secretion and rescue mutant factor VIII in mice with hemophilia Avon Willebrand factor: more than a regulator of hemostasis and thrombosis.Identification and functional analysis of a novel von Willebrand factor mutation in a family with type 2A von Willebrand disease.Characterization of zebrafish von Willebrand factor reveals conservation of domain structure, multimerization, and intracellular storage.Cellular and molecular basis of von Willebrand disease: studies on blood outgrowth endothelial cells.Insights into pathological mechanisms of missense mutations in C-terminal domains of von Willebrand factor causing qualitative or quantitative von Willebrand disease.Discrepant platelet and plasma von Willebrand factor in von Willebrand disease patients with p.Pro2808Leufs*24.Angiodysplasia in von Willebrand Disease: Understanding the Clinical and Basic Science.Biogenesis of Weibel-Palade bodies in von Willebrand's disease variants with impaired von Willebrand factor intrachain or interchain disulfide bond formation.Enhanced assay of endothelial exocytosis using extracellular matrix componentsClinical phenotype in genetically confirmed von Willebrand disease type 2N patients reflects a haemophilia A phenotype.A common mechanism by which type 2A von Willebrand disease mutations enhance ADAMTS13 proteolysis revealed with a von Willebrand factor A2 domain FRET construct.Formation of platelet-binding von Willebrand factor strings on non-endothelial cells.Quantitative microscopy of mole rat eosinophil granule morphology.Mutations in the D'D3 region of VWF traditionally associated with type 1 VWD lead to quantitative and qualitative deficiencies of VWF.Storage and secretion of naturally occurring von Willebrand factor A domain variants
P2860
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P2860
Intracellular storage and regulated secretion of von Willebrand factor in quantitative von Willebrand disease
description
2011 nî lūn-bûn
@nan
2011年の論文
@ja
2011年論文
@yue
2011年論文
@zh-hant
2011年論文
@zh-hk
2011年論文
@zh-mo
2011年論文
@zh-tw
2011年论文
@wuu
2011年论文
@zh
2011年论文
@zh-cn
name
Intracellular storage and regu ...... itative von Willebrand disease
@en
type
label
Intracellular storage and regu ...... itative von Willebrand disease
@en
prefLabel
Intracellular storage and regu ...... itative von Willebrand disease
@en
P2093
P2860
P50
P356
P1476
Intracellular storage and regu ...... itative von Willebrand disease
@en
P2093
Hetty C de Boer
Karine M Valentijn
Pieter H Reitsma
P2860
P304
24180-24188
P356
10.1074/JBC.M110.215194
P407
P50
P577
2011-05-19T00:00:00Z