Batten's disease: clues to neuronal protein catabolism in lysosomes
about
Antisense palmitoyl protein thioesterase 1 (PPT1) treatment inhibits PPT1 activity and increases cell death in LA-N-5 neuroblastoma cellsBiosynthetic processing of cathepsins and lysosomal degradation are abolished in asparaginyl endopeptidase-deficient miceAutophagy as a regulated pathway of cellular degradationMetabolic profiles to define the genome: can we hear the phenotypes?Function, therapeutic potential and cell biology of BACE proteases: current status and future prospects.Looking chloride channels straight in the eye: bestrophins, lipofuscinosis, and retinal degeneration.Clearing the brain's cobwebs: the role of autophagy in neuroprotectionNeuronal pigmented autophagic vacuoles: lipofuscin, neuromelanin, and ceroid as macroautophagic responses during aging and disease.Vitamin E deficiency and metabolic deficits in neuronal ceroid lipofuscinosis described by bioinformatics.Profound infantile neuroretinal dysfunction in a heterozygote for the CLN3 genetic defect.CLC-3 deficiency leads to phenotypes similar to human neuronal ceroid lipofuscinosis.Characterisation of lipofuscin-like lysosomal inclusion bodies from human placenta.
P2860
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P2860
Batten's disease: clues to neuronal protein catabolism in lysosomes
description
2000 nî lūn-bûn
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2000 թուականի Ապրիլին հրատարակուած գիտական յօդուած
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2000 թվականի ապրիլին հրատարակված գիտական հոդված
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2000年の論文
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2000年論文
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2000年論文
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2000年論文
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2000年論文
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2000年論文
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2000年论文
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name
Batten's disease: clues to neuronal protein catabolism in lysosomes
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Batten's disease: clues to neuronal protein catabolism in lysosomes
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Batten's disease: clues to neuronal protein catabolism in lysosomes
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Batten's disease: clues to neuronal protein catabolism in lysosomes
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type
label
Batten's disease: clues to neuronal protein catabolism in lysosomes
@ast
Batten's disease: clues to neuronal protein catabolism in lysosomes
@en
Batten's disease: clues to neuronal protein catabolism in lysosomes
@en-gb
Batten's disease: clues to neuronal protein catabolism in lysosomes
@nl
prefLabel
Batten's disease: clues to neuronal protein catabolism in lysosomes
@ast
Batten's disease: clues to neuronal protein catabolism in lysosomes
@en
Batten's disease: clues to neuronal protein catabolism in lysosomes
@en-gb
Batten's disease: clues to neuronal protein catabolism in lysosomes
@nl
P2860
P921
P1476
Batten's disease: clues to neuronal protein catabolism in lysosomes
@en
P2860
P304
P356
10.1002/(SICI)1097-4547(20000415)60:2<133::AID-JNR1>3.0.CO;2-3
P407
P577
2000-04-15T00:00:00Z