Molecular mechanism for regulation of the human mitochondrial branched-chain alpha-ketoacid dehydrogenase complex by phosphorylation
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Characterization of testis-specific isoenzyme of human pyruvate dehydrogenaseStructural basis for inactivation of the human pyruvate dehydrogenase complex by phosphorylation: role of disordered phosphorylation loopsThe two active sites in human branched-chain alpha-keto acid dehydrogenase operate independently without an obligatory alternating-site mechanismStructural and Biochemical Characterization of Human Mitochondrial Branched-chain -Ketoacid Dehydrogenase PhosphatasePhosphorylation regulates assembly of the caspase-6 substrate-binding groove.Benzothiophene carboxylate derivatives as novel allosteric inhibitors of branched-chain α-ketoacid dehydrogenase kinaseStructure-based design and mechanisms of allosteric inhibitors for mitochondrial branched-chain α-ketoacid dehydrogenase kinase.Two novel mutations in the BCKDK (branched-chain keto-acid dehydrogenase kinase) gene are responsible for a neurobehavioral deficit in two pediatric unrelated patientsBCKDH: the missing link in apicomplexan mitochondrial metabolism is required for full virulence of Toxoplasma gondii and Plasmodium bergheiDual specificity phosphatases 18 and 21 target to opposing sides of the mitochondrial inner membraneBranched-chain amino acid metabolon: interaction of glutamate dehydrogenase with the mitochondrial branched-chain aminotransferase (BCATm)Inferring high-confidence human protein-protein interactionsPhenylbutyrate therapy for maple syrup urine disease.Genetic Predisposition to an Impaired Metabolism of the Branched-Chain Amino Acids and Risk of Type 2 Diabetes: A Mendelian Randomisation Analysis.CLC anion channel regulatory phosphorylation and conserved signal transduction domainsRole of Na+ and K+ in enzyme function.Conformational ensemble modulates cooperativity in the rate-determining catalytic step in the E1 component of the Escherichia coli pyruvate dehydrogenase multienzyme complex.MnSOD in oxidative stress response-potential regulation via mitochondrial protein influx.Nuclear magnetic resonance approaches in the study of 2-oxo acid dehydrogenase multienzyme complexes--a literature review.Molecular Mechanisms of Enzyme Activation by Monovalent Cations.Determination of pre-steady-state rate constants on the Escherichia coli pyruvate dehydrogenase complex reveals that loop movement controls the rate-limiting step.Synthesis and conformational analysis of stevastelin C3 analogues and their activity against the dual-specific vaccina H1-related phosphatase.Lipoic acid metabolism and mitochondrial redox regulation.BCAA Metabolism and NH3 Homeostasis.A thiamin-bound, pre-decarboxylation reaction intermediate analogue in the pyruvate dehydrogenase E1 subunit induces large scale disorder-to-order transformations in the enzyme and reveals novel structural features in the covalently bound adduct.BCKDK phosphorylates BCKDHSilico analysis of a novel mutation c.550delT in a Chinese patient with maple syrup urine diseaseFourteen new mutations of , and genes associated with maple syrup urine disease (MSUD) in Malaysian population
P2860
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P2860
Molecular mechanism for regulation of the human mitochondrial branched-chain alpha-ketoacid dehydrogenase complex by phosphorylation
description
2004 nî lūn-bûn
@nan
2004 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2004 թվականի դեկտեմբերին հրատարակված գիտական հոդված
@hy
2004年の論文
@ja
2004年論文
@yue
2004年論文
@zh-hant
2004年論文
@zh-hk
2004年論文
@zh-mo
2004年論文
@zh-tw
2004年论文
@wuu
name
Molecular mechanism for regula ...... ase complex by phosphorylation
@ast
Molecular mechanism for regula ...... ase complex by phosphorylation
@en
Molecular mechanism for regula ...... ase complex by phosphorylation
@en-gb
Molecular mechanism for regula ...... ase complex by phosphorylation
@nl
type
label
Molecular mechanism for regula ...... ase complex by phosphorylation
@ast
Molecular mechanism for regula ...... ase complex by phosphorylation
@en
Molecular mechanism for regula ...... ase complex by phosphorylation
@en-gb
Molecular mechanism for regula ...... ase complex by phosphorylation
@nl
prefLabel
Molecular mechanism for regula ...... ase complex by phosphorylation
@ast
Molecular mechanism for regula ...... ase complex by phosphorylation
@en
Molecular mechanism for regula ...... ase complex by phosphorylation
@en-gb
Molecular mechanism for regula ...... ase complex by phosphorylation
@nl
P2093
P1433
P1476
Molecular mechanism for regula ...... ase complex by phosphorylation
@en
P2093
David T Chuang
Jacinta L Chuang
Masato Kato
R Max Wynn
P304
P356
10.1016/J.STR.2004.09.013
P407
P577
2004-12-01T00:00:00Z