Pre-symptomatic activation of antioxidant responses and alterations in glucose and pyruvate metabolism in Niemann-Pick Type C1-deficient murine brain
about
Adaptations of energy metabolism associated with increased levels of mitochondrial cholesterol in Niemann-Pick type C1-deficient cells.Niemann-Pick C disease and mobilization of lysosomal cholesterol by cyclodextrinQuantitative Proteomics of Human Fibroblasts with I1061T Mutation in Niemann-Pick C1 (NPC1) Protein Provides Insights into the Disease Pathogenesis.Sphingolipids and mitochondrial function, lessons learned from yeastSphingolipids and mitochondrial function in budding yeast.Alcohol Withdrawal and Cerebellar Mitochondria.Mitochondrial cholesterol: mechanisms of import and effects on mitochondrial function.NMR analysis reveals significant differences in the plasma metabolic profiles of Niemann Pick C1 patients, heterozygous carriers, and healthy controls.Vitamin E dietary supplementation improves neurological symptoms and decreases c-Abl/p73 activation in Niemann-Pick C miceRoutes and mechanisms of post-endosomal cholesterol trafficking: A story that never ends.Linking mitochondrial dysfunction to neurodegeneration in lysosomal storage diseases.Role of Diffusion Tensor Imaging in Prognostication and Treatment Monitoring in Niemann-Pick Disease Type C1.Measurement of Mitochondrial Cholesterol Import Using a Mitochondria-Targeted CYP11A1 Fusion Construct.Quantitative Analysis of the Proteome Response to the Histone Deacetylase Inhibitor (HDACi) Vorinostat in Niemann-Pick Type C1 disease.Evaluation of Two Liver Treatment Strategies in a Mouse Model of Niemann-Pick-Disease Type C1.Olfactory Performance as an Indicator for Protective Treatment Effects in an Animal Model of Neurodegeneration
P2860
Q33718519-83169AD4-0719-4CE2-B15F-8367576CA708Q33945068-3361193A-229C-4926-B3CA-4AE7BBA4FB6FQ36103923-F2FD9262-DDBE-44D4-99D5-E3C4C36EA853Q37698292-C8994214-741D-47CC-AB65-CB46BBD803A5Q38224024-203CA732-3CDA-4943-A4AE-F14622E75306Q38246642-2F9562F6-7386-4922-9FB2-EE914BBA5098Q38271508-2C3CD494-A799-46B6-B131-F739FC15D140Q38652409-0CCE4DC4-A34E-482B-8E38-62E3A842A340Q38969914-904D0E6F-9AA7-4120-BE22-0024D34BA7E0Q39133252-A7F91376-410C-4936-B482-71DA619D042DQ39287167-467C4EC2-1609-464A-9A90-2B78F2F7F38FQ42112277-6BC17B80-DA94-484A-9426-39D98A1C62D7Q46088272-28346076-74FF-46C0-BFE1-88CADA374FF4Q46094394-B7D4AF99-D75F-4844-92B2-7BA9627AA04EQ51731168-8A7C21CA-2469-4FD5-A606-1586A2BC2EDDQ58781637-32E15CE2-CF83-49CF-9BEB-F0F20B577DDA
P2860
Pre-symptomatic activation of antioxidant responses and alterations in glucose and pyruvate metabolism in Niemann-Pick Type C1-deficient murine brain
description
2013 nî lūn-bûn
@nan
2013 թուականին հրատարակուած գիտական յօդուած
@hyw
2013 թվականին հրատարակված գիտական հոդված
@hy
2013年の論文
@ja
2013年論文
@yue
2013年論文
@zh-hant
2013年論文
@zh-hk
2013年論文
@zh-mo
2013年論文
@zh-tw
2013年论文
@wuu
name
Pre-symptomatic activation of ...... Type C1-deficient murine brain
@ast
Pre-symptomatic activation of ...... Type C1-deficient murine brain
@en
Pre-symptomatic activation of ...... Type C1-deficient murine brain
@nl
type
label
Pre-symptomatic activation of ...... Type C1-deficient murine brain
@ast
Pre-symptomatic activation of ...... Type C1-deficient murine brain
@en
Pre-symptomatic activation of ...... Type C1-deficient murine brain
@nl
prefLabel
Pre-symptomatic activation of ...... Type C1-deficient murine brain
@ast
Pre-symptomatic activation of ...... Type C1-deficient murine brain
@en
Pre-symptomatic activation of ...... Type C1-deficient murine brain
@nl
P2093
P2860
P1433
P1476
Pre-symptomatic activation of ...... Type C1-deficient murine brain
@en
P2093
Barbara Karten
Barry E Kennedy
Debra Fice
Ian Burton
Tiffany M Mailman
Veronique G LeBlanc
P2860
P304
P356
10.1371/JOURNAL.PONE.0082685
P407
P577
2013-01-01T00:00:00Z