Murine muscle cell models for Pompe disease and their use in studying therapeutic approaches

Murine muscle cell models for Pompe disease and their use in studying therapeutic approaches

Item
http://www.wikidata.org/entity/Q24647307
Mending a broken heart: the role of mitophagy in cardioprotectionRole of autophagy in glycogen breakdown and its relevance to chloroquine myopathyThe pharmacological chaperone AT2220 increases the specific activity and lysosomal delivery of mutant acid alpha-glucosidase, and promotes glycogen reduction in a transgenic mouse model of Pompe diseaseMicroautophagy: lesser-known self-eating.Suppression of mTORC1 activation in acid-α-glucosidase-deficient cells and mice is ameliorated by leucine supplementation.Suppression of autophagy permits successful enzyme replacement therapy in a lysosomal storage disorder--murine Pompe disease.Untangling autophagy measurements: all fluxed up.Pompe disease results in a Golgi-based glycosylation deficit in human induced pluripotent stem cell-derived cardiomyocytes.This old heart: Cardiac aging and autophagy.Defects in calcium homeostasis and mitochondria can be reversed in Pompe disease.Phosphorylation of the insulin receptor by AMP-activated protein kinase (AMPK) promotes ligand-independent activation of the insulin signalling pathway in rodent muscleTranscription factor EB (TFEB) is a new therapeutic target for Pompe diseaseWITHDRAWN: Clearance of lysosomal glycogen accumulation by Transcription factor EB (TFEB) in muscle cells from lysosomal alpha-glucosidase deficient mice."Get the Balance Right": Pathological Significance of Autophagy Perturbation in Neuromuscular DisordersModulation of mTOR signaling as a strategy for the treatment of Pompe disease.A Skeletal Muscle Model of Infantile-onset Pompe Disease with Patient-specific iPS CellsHuman Pompe disease-induced pluripotent stem cells for pathogenesis modeling, drug testing and disease marker identification.
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Murine muscle cell models for Pompe disease and their use in studying therapeutic approaches

Item
http://www.wikidata.org/entity/Q24647307
description
2009 nî lūn-bûn
@nan
2009 թուականի Ապրիլին հրատարակուած գիտական յօդուած
@hyw
2009 թվականի ապրիլին հրատարակված գիտական հոդված
@hy
2009年の論文
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2009年論文
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2009年論文
@zh-hant
2009年論文
@zh-hk
2009年論文
@zh-mo
2009年論文
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2009年论文
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Murine muscle cell models for ...... tudying therapeutic approaches
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Murine muscle cell models for ...... tudying therapeutic approaches
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Murine muscle cell models for ...... tudying therapeutic approaches
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Murine muscle cell models for ...... tudying therapeutic approaches
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Murine muscle cell models for ...... tudying therapeutic approaches
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Murine muscle cell models for ...... tudying therapeutic approaches
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Murine muscle cell models for ...... tudying therapeutic approaches
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Murine muscle cell models for ...... tudying therapeutic approaches
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Murine muscle cell models for ...... tudying therapeutic approaches
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Murine muscle cell models for ...... tudying therapeutic approaches
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10.1016/J.YMGME.2008.12.012
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