about
Murine muscle cell models for Pompe disease and their use in studying therapeutic approachesMyocardial autophagic energy stress responses--macroautophagy, mitophagy, and glycophagyEffects of lysosomal membrane protein depletion on the Salmonella-containing vacuole.VCP associated inclusion body myopathy and paget disease of bone knock-in mouse model exhibits tissue pathology typical of human disease.Inclusion body myopathy, Paget's disease of the bone and fronto-temporal dementia: a disorder of autophagyLAMP2 microdeletions in patients with Danon disease.Arginine68 is an essential residue for the C-terminal cleavage of human Atg8 family proteinsGlobal gene expression profiling in R155H knock-in murine model of VCP disease.Autophagic stress in neuronal injury and disease.Molecular and cellular mechanisms of skeletal muscle atrophy: an update.Human NK cell lytic granules and regulation of their exocytosisA progressive translational mouse model of human valosin-containing protein disease: the VCP(R155H/+) mouseImpaired protein aggregate handling and clearance underlie the pathogenesis of p97/VCP-associated disease.Suppression of autophagy in skeletal muscle uncovers the accumulation of ubiquitinated proteins and their potential role in muscle damage in Pompe disease.Danon disease as a cause of autophagic vacuolar myopathy.Monitoring autophagy in lysosomal storage disordersDefects of Vps15 in skeletal muscles lead to autophagic vacuolar myopathy and lysosomal diseaseRole for LAMP-2 in endosomal cholesterol transport.Valosin containing protein associated inclusion body myopathy: abnormal vacuolization, autophagy and cell fusion in myoblastsDanon disease: a phenotypic expression of LAMP-2 deficiency.Myocardial glycogen dynamics: new perspectives on disease mechanisms.Overexpression of microRNA-96-5p inhibits autophagy and apoptosis and enhances the proliferation, migration and invasiveness of human breast cancer cells.Influence of the programmed cell death of lymphocytes on the immunity of patients with atopic bronchial asthma.Increased vulnerability with aging to MPTP: the mechanisms underlying mitochondrial dynamics.Conditional knockout of pik3c3 causes a murine muscular dystrophy.Diagnostic challenges for Pompe disease: an under-recognized cause of floppy baby syndrome.Induction of autophagy through the activating transcription factor 4 (ATF4)-dependent amino acid response pathway in maternal skeletal muscle may function as the molecular memory in response to gestational protein restriction to alert offspring to mEZH2 inhibitors transcriptionally upregulate cytotoxic autophagy and cytoprotective unfolded protein response in human colorectal cancer cells.Autophagic vacuoles with sarcolemmal features delineate Danon disease and related myopathies.Runx1 prevents wasting, myofibrillar disorganization, and autophagy of skeletal muscle.Apobec2 deficiency causes mitochondrial defects and mitophagy in skeletal muscle.Autophagic degeneration of motor neurons in a model of slow glutamate excitotoxicity in vitro.Dysregulation of autophagy as a common mechanism in lysosomal storage diseases.ALS-Associated Endoplasmic Reticulum Proteins in Denervated Skeletal Muscle: Implications for Motor Neuron Disease Pathology.Mechanisms and function of autophagy in intestinal disease.Autophagy: An Alternative Degradation Mechanism for Misfolded ProteinsAutophagy Mechanism, Regulation, Functions, and Disorders
P2860
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P2860
description
2003 nî lūn-bûn
@nan
2003 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2003 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2003年の論文
@ja
2003年学术文章
@wuu
2003年学术文章
@zh-cn
2003年学术文章
@zh-hans
2003年学术文章
@zh-my
2003年学术文章
@zh-sg
2003年學術文章
@yue
name
Autophagic vacuolar myopathies.
@ast
Autophagic vacuolar myopathies.
@en
type
label
Autophagic vacuolar myopathies.
@ast
Autophagic vacuolar myopathies.
@en
prefLabel
Autophagic vacuolar myopathies.
@ast
Autophagic vacuolar myopathies.
@en
P1476
Autophagic vacuolar myopathies.
@en
P2093
Ichizo Nishino
P2860
P2888
P356
10.1007/S11910-003-0040-Y
P577
2003-01-01T00:00:00Z