about
Huntingtin interacting proteins are genetic modifiers of neurodegenerationPalmitoyl protein thioesterase-1 deficiency impairs synaptic vesicle recycling at nerve terminals, contributing to neuropathology in humans and miceAge-dependent alterations of corticostriatal activity in the YAC128 mouse model of Huntington diseaseAsialoerythropoietin is not effective in the R6/2 line of Huntington's disease miceIron dysregulation in Huntington's diseaseSynaptopathies: synaptic dysfunction in neurological disorders - A review from students to studentsNo longer falling on deaf ears: mechanisms of degeneration and regeneration of cochlear ribbon synapses.Normal huntingtin function: an alternative approach to Huntington's diseaseApolipoprotein E-mimetics inhibit neurodegeneration and restore cognitive functions in a transgenic Drosophila model of Alzheimer's diseaseProgressive synaptic pathology of motor cortical neurons in a BAC transgenic mouse model of Huntington's disease.TDAG51 mediates the effects of insulin-like growth factor I (IGF-I) on cell survival.Comparative study of human and mouse postsynaptic proteomes finds high compositional conservation and abundance differences for key synaptic proteinsWild-type but not mutant huntingtin modulates the transcriptional activity of liver X receptorsLoss of SNAP-25 and rabphilin 3a in sensory-motor cortex in Huntington's disease.Early Hippocampal Synaptic Loss Precedes Neuronal Loss and Associates with Early Behavioural Deficits in Three Distinct Strains of Prion Disease.Activated microglia proliferate at neurites of mutant huntingtin-expressing neuronsGenetic modifiers of Drosophila palmitoyl-protein thioesterase 1-induced degeneration.Staying connected: synapses in Alzheimer disease.Repeat instability: mechanisms of dynamic mutations.Therapeutics development for triplet repeat expansion diseases.Molecular neuropathology of the synapse in sheep with CLN5 Batten diseaseThe use of the R6 transgenic mouse models of Huntington's disease in attempts to develop novel therapeutic strategies.Suppression of neurodegeneration and increased neurotransmission caused by expanded full-length huntingtin accumulating in the cytoplasmThe corticostriatal pathway in Huntington's disease.Investigating complex I deficiency in Purkinje cells and synapses in patients with mitochondrial diseaseA large number of protein expression changes occur early in life and precede phenotype onset in a mouse model for huntington disease.GDNF control of the glutamatergic cortico-striatal pathway requires tonic activation of adenosine A receptors.Loss of Hsp70 exacerbates pathogenesis but not levels of fibrillar aggregates in a mouse model of Huntington's disease.GluN3A: an NMDA receptor subunit with exquisite properties and functions.Suppressing aberrant GluN3A expression rescues synaptic and behavioral impairments in Huntington's disease models.Could Perinatal Asphyxia Induce a Synaptopathy? New Highlights from an Experimental Model.Genetic mouse models of Huntington's disease: focus on electrophysiological mechanisms.Stimulated emission depletion (STED) microscopy reveals nanoscale defects in the developmental trajectory of dendritic spine morphogenesis in a mouse model of fragile X syndrome.Huntington's disease and Group I metabotropic glutamate receptors.Barfly: sculpting membranes at the Drosophila neuromuscular junction.Pathophysiology of Huntington's disease: time-dependent alterations in synaptic and receptor function.Selective vulnerability of synaptic signaling and metabolism to nitrosative stressGene expression profiling and therapeutic interventions in neurodegenerative diseases: a comprehensive study on potentiality and limits.Mechanisms underlying synaptic vulnerability and degeneration in neurodegenerative disease.Metabotropic glutamate receptor 5 as a potential therapeutic target in Huntington's disease.
P2860
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P2860
description
2003 nî lūn-bûn
@nan
2003 թուականի Հոկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2003 թվականի հոտեմբերին հրատարակված գիտական հոդված
@hy
2003年の論文
@ja
2003年論文
@yue
2003年論文
@zh-hant
2003年論文
@zh-hk
2003年論文
@zh-mo
2003年論文
@zh-tw
2003年论文
@wuu
name
Huntington's disease: a synaptopathy?
@ast
Huntington's disease: a synaptopathy?
@en
type
label
Huntington's disease: a synaptopathy?
@ast
Huntington's disease: a synaptopathy?
@en
prefLabel
Huntington's disease: a synaptopathy?
@ast
Huntington's disease: a synaptopathy?
@en
P1476
Huntington's disease: a synaptopathy?
@en
P2093
Markus Plomann
P304
P356
10.1016/J.MOLMED.2003.08.006
P577
2003-10-01T00:00:00Z