about
The genetic epidemiology of neurodegenerative disease.Neuroprotective effect of Nrf2/ARE activators, CDDO ethylamide and CDDO trifluoroethylamide, in a mouse model of amyotrophic lateral sclerosisMolecular motor proteins and amyotrophic lateral sclerosisRedox regulation in amyotrophic lateral sclerosisCo-induction of the heat shock response ameliorates disease progression in a mouse model of human spinal and bulbar muscular atrophy: implications for therapyInclusion body myopathy associated with Paget disease of bone and frontotemporal dementia is caused by mutant valosin-containing proteinZinc binding modulates the entire folding free energy surface of human Cu,Zn superoxide dismutase.Protein nitration in a mouse model of familial amyotrophic lateral sclerosis: possible multifunctional role in the pathogenesis.Characterization of detergent-insoluble proteins in ALS indicates a causal link between nitrative stress and aggregation in pathogenesis.Accumulation of wildtype and ALS-linked mutated VAPB impairs activity of the proteasome.No widespread induction of cell death genes occurs in pure motoneurons in an amyotrophic lateral sclerosis mouse model.Protein aggregation and protein instability govern familial amyotrophic lateral sclerosis patient survival.Reversal of amyloid-induced heart disease in desmin-related cardiomyopathy.Neurodegenerative models in Drosophila: polyglutamine disorders, Parkinson disease, and amyotrophic lateral sclerosis.Dysfunction of endocytic kinase AAK1 in ALSArimoclomol: a potential therapy under development for ALS.Superoxide dismutases and superoxide reductases.Protective and Toxic Neuroinflammation in Amyotrophic Lateral Sclerosis.The nuclear factor kappaB-activator gene PLEKHG5 is mutated in a form of autosomal recessive lower motor neuron disease with childhood onset.Role of molecular chaperones in neurodegenerative disorders.Golgi fragmentation in amyotrophic lateral sclerosis, an overview of possible triggers and consequences.Escherichia coli ClpB is a non-processive polypeptide translocase.Role of oxidative stress in refractory epilepsy: evidence in patients and experimental models.Motor neuron degeneration in a mouse model of seipinopathy.Emerging disease-modifying therapies for the treatment of motor neuron disease/amyotropic lateral sclerosis.The wobbler mouse, an ALS animal model.Comparative Analysis of VOCs in Exhaled Breath of Amyotrophic Lateral Sclerosis and Cervical Spondylotic Myelopathy PatientsNeurotrophic Peptides: Potential Drugs for Treatment of Amyotrophic Lateral Sclerosis and Alzheimer's diseaseEarly steps in thermal unfolding of superoxide dismutase 1 are similar to the conformational changes associated with the ALS-associated A4V mutation.A quantitative examination of the role of cargo-exerted forces in axonal transportFolding of human superoxide dismutase: disulfide reduction prevents dimerization and produces marginally stable monomersBiomarkers in amyotrophic lateral sclerosis: opportunities and limitations.Molecular pathways of motor neuron injury in amyotrophic lateral sclerosis.Understanding ALS: new therapeutic approaches.Optineurin and amyotrophic lateral sclerosis.ER stress and unfolded protein response in amyotrophic lateral sclerosis-a controversial role of protein disulphide isomerase.Cell stress induces TDP-43 pathological changes associated with ERK1/2 dysfunction: implications in ALS.Experimental models for the study of neurodegeneration in amyotrophic lateral sclerosis.Characterization of Wnt/β-catenin and BMP/Smad signaling pathways in an in vitro model of amyotrophic lateral sclerosis.Is the spinal cord motoneuron exclusively a target in ALS? Comparison between astroglial reactivity in a rat model of familial ALS and in human sporadic ALS cases.
P2860
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P2860
description
2003 nî lūn-bûn
@nan
2003年の論文
@ja
2003年論文
@yue
2003年論文
@zh-hant
2003年論文
@zh-hk
2003年論文
@zh-mo
2003年論文
@zh-tw
2003年论文
@wuu
2003年论文
@zh
2003年论文
@zh-cn
name
Protein aggregation in motor neurone disorders.
@ast
Protein aggregation in motor neurone disorders.
@en
type
label
Protein aggregation in motor neurone disorders.
@ast
Protein aggregation in motor neurone disorders.
@en
prefLabel
Protein aggregation in motor neurone disorders.
@ast
Protein aggregation in motor neurone disorders.
@en
P2860
P1476
Protein aggregation in motor neurone disorders
@en
P2093
T P Beaujeux
P2860
P304
P356
10.1046/J.0305-1846.2003.00518.X
P577
2003-12-01T00:00:00Z