Carbohydrate structures of recombinant human alpha-L-iduronidase secreted by Chinese hamster ovary cells.
about
NPC2, the protein deficient in Niemann-Pick C2 disease, consists of multiple glycoforms that bind a variety of sterolsInsights into mucopolysaccharidosis I from the structure and action of α-L-iduronidaseHuman α-l-iduronidase uses its own N -glycan as a substrate-binding and catalytic moduleGenotypic and bioinformatic evaluation of the alpha-l-iduronidase gene and protein in patients with mucopolysaccharidosis type I from Colombia, Ecuador and Peru.Reprogramming erythroid cells for lysosomal enzyme production leads to visceral and CNS cross-correction in mice with Hurler syndrome.Glycan microarray analysis of P-type lectins reveals distinct phosphomannose glycan recognitionCarbohydrate analysis throughout the development of a protein therapeutic.Lipoprotein receptor binding, cellular uptake, and lysosomal delivery of fusions between the receptor-associated protein (RAP) and alpha-L-iduronidase or acid alpha-glucosidase.Enzymes approved for human therapy: indications, mechanisms and adverse effects.Biosynthesis, glycosylation, and enzymatic processing in vivo of human tripeptidyl-peptidase I.High-dose enzyme replacement therapy in murine Hurler syndromeCharacterization and downstream mannose phosphorylation of human recombinant α-L-iduronidase produced in Arabidopsis complex glycan-deficient (cgl) seedsSpp24 derivatives stimulate a Gi-protein coupled receptor-Erk1/2 signaling pathway and modulate gene expressions in W-20-17 cells.N-glycan structures and downstream mannose-phosphorylation of plant recombinant human alpha-L-iduronidase: toward development of enzyme replacement therapy for mucopolysaccharidosis I.Influence of an ER-retention signal on the N-glycosylation of recombinant human α-L-iduronidase generated in seeds of Arabidopsis.Molecular characterization of acidic peptide:N-glycanase from the dimorphic yeast Yarrowia lipolytica.
P2860
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P2860
Carbohydrate structures of recombinant human alpha-L-iduronidase secreted by Chinese hamster ovary cells.
description
1997 nî lūn-bûn
@nan
1997年の論文
@ja
1997年論文
@yue
1997年論文
@zh-hant
1997年論文
@zh-hk
1997年論文
@zh-mo
1997年論文
@zh-tw
1997年论文
@wuu
1997年论文
@zh
1997年论文
@zh-cn
name
Carbohydrate structures of rec ...... y Chinese hamster ovary cells.
@en
type
label
Carbohydrate structures of rec ...... y Chinese hamster ovary cells.
@en
prefLabel
Carbohydrate structures of rec ...... y Chinese hamster ovary cells.
@en
P2093
P2860
P356
P1476
Carbohydrate structures of rec ...... y Chinese hamster ovary cells.
@en
P2093
P2860
P304
22758-22765
P356
10.1074/JBC.272.36.22758
P407
P577
1997-09-01T00:00:00Z