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Dystrophin protects the sarcolemma from stresses developed during muscle contraction

Dystrophin protects the sarcolemma from stresses developed during muscle contraction

http://www.wikidata.org/entity/Q36259954

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Skeletal muscle laminin and MDC1A: pathogenesis and treatment strategies.Corticosteroids for the treatment of Duchenne muscular dystrophy Calcium antagonists for Duchenne muscular dystrophy Glucocorticoid corticosteroids for Duchenne muscular dystrophy The phosphoinositol 3,4-bisphosphate-binding protein TAPP1 interacts with syntrophins and regulates actin cytoskeletal organization Functional defects of a muscle-specific calpain, p94, caused by mutations associated with limb-girdle muscular dystrophy type 2A Mouse fukutin deletion impairs dystroglycan processing and recapitulates muscular dystrophy Role of telomere dysfunction in cardiac failure in Duchenne muscular dystrophy Automated drug screening with contractile muscle tissue engineered from dystrophic myoblasts Short telomeres and stem cell exhaustion model Duchenne muscular dystrophy in mdx/mTR mice Viral mediated expression of insulin-like growth factor I blocks the aging-related loss of skeletal muscle function Investigation of Debio 025, a cyclophilin inhibitor, in the dystrophic mdx mouse, a model for Duchenne muscular dystrophy Diacylglycerol kinase-zeta localization in skeletal muscle is regulated by phosphorylation and interaction with syntrophins Sildenafil and cardiomyocyte-specific cGMP signaling prevent cardiomyopathic changes associated with dystrophin deficiency Mechanotransduction in skeletal muscle Mechanosensitive channel properties and membrane mechanics in mouse dystrophic myotubes Down-regulation of a novel actin-binding molecule, skeletrophin, in malignant melanoma Brain dystrophin-glycoprotein complex: persistent expression of beta-dystroglycan, impaired oligomerization of Dp71 and up-regulation of utrophins in animal models of muscular dystrophy Muscle regeneration in dystrophin-deficient mdx mice studied by gene expression profiling Metabogenic and Nutriceutical Approaches to Address Energy Dysregulation and Skeletal Muscle Wasting in Duchenne Muscular Dystrophy A muscle stem cell for every muscle: variability of satellite cell biology among different muscle groups Dystrophin and the two related genetic diseases, Duchenne and Becker muscular dystrophies Cardiac involvement in Duchenne and Becker muscular dystrophy Advancements in stem cells treatment of skeletal muscle wasting The potential of sarcospan in adhesion complex replacement therapeutics for the treatment of muscular dystrophy Multi-parametric MRI at 14T for muscular dystrophy mice treated with AAV vector-mediated gene therapy Rescue of dystrophic skeletal muscle by PGC-1α involves a fast to slow fiber type shift in the mdx mouse Low intensity, high frequency vibration training to improve musculoskeletal function in a mouse model of Duchenne muscular dystrophy The burrowing behavior of the nematode Caenorhabditis elegans: a new assay for the study of neuromuscular disorders Inhibitory control over Ca(2+) sparks via mechanosensitive channels is disrupted in dystrophin deficient muscle but restored by mini-dystrophin expression Current understanding of molecular pathology and treatment of cardiomyopathy in duchenne muscular dystrophy Genetic evidence in the mouse solidifies the calcium hypothesis of myofiber death in muscular dystrophy Hanging on for the ride: adhesion to the extracellular matrix mediates cellular responses in skeletal muscle morphogenesis and disease Expression of gamma -sarcoglycan in smooth muscle and its interaction with the smooth muscle sarcoglycan-sarcospan complex Sarcoglycan isoforms in skeletal muscle The dystrophin complex forms a mechanically strong link between the sarcolemma and costameric actin Interaction of gamma 1-syntrophin with diacylglycerol kinase-zeta. Regulation of nuclear localization by PDZ interactions The WW domain of dystrophin requires EF-hands region to interact with beta-dystroglycan Cytoplasmic gamma-actin expression in diverse animal models of muscular dystrophy Biomechanics of the sarcolemma and costameres in single skeletal muscle fibers from normal and dystrophin-null mice

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P2860

Dystrophin protects the sarcolemma from stresses developed during muscle contraction

http://www.wikidata.org/entity/Q36259954

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1993 nî lūn-bûn

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1993年の論文

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1993年学术文章

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1993年学术文章

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1993年学术文章

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1993年学术文章

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1993年学术文章

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1993年學術文章

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1993年學術文章

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1993年學術文章

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name

Dystrophin protects the sarcolemma from stresses developed during muscle contraction

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Dystrophin protects the sarcolemma from stresses developed during muscle contraction

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Dystrophin protects the sarcolemma from stresses developed during muscle contraction

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Dystrophin protects the sarcolemma from stresses developed during muscle contraction

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Dystrophin protects the sarcolemma from stresses developed during muscle contraction

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Proceedings of the National Academy of Sciences of the United States of America

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Dystrophin protects the sarcolemma from stresses developed during muscle contraction

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A M Kelly

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B J Petrof

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H H Stedman

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H L Sweeney

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J B Shrager

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P2860

The complete sequence of dystrophin predicts a rod-shaped cytoskeletal protein

Deficiency of the 50K dystrophin-associated glycoprotein in severe childhood autosomal recessive muscular dystrophy

Primary structure of dystrophin-associated glycoproteins linking dystrophin to the extracellular matrix

Membrane organization of the dystrophin-glycoprotein complex

Dystrophin: the protein product of the Duchenne muscular dystrophy locus

Complete cloning of the duchenne muscular dystrophy (DMD) cDNA and preliminary genomic organization of the DMD gene in normal and affected individuals

Decreased osmotic stability of dystrophin-less muscle cells from the mdx mouse.

Reductions of erythrocyte membrane viscoelastic coefficients reflect spectrin deficiencies in hereditary spherocytosis.

Severe childhood muscular dystrophy affecting both sexes and frequent in Tunisia.

Studies of sarcolemmal integrity in myopathic muscle.

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3710-3714

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8

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90

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8475120

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46371

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