Phenylbutyrate up-regulates the adrenoleukodystrophy-related gene as a nonclassical peroxisome proliferator
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Current and future pharmacological treatment strategies in X-linked adrenoleukodystrophyFunctional Rescue of Trafficking-Impaired ABCB4 Mutants by Chemical ChaperonesFunctional Characterization of IPSC-Derived Brain Cells as a Model for X-Linked AdrenoleukodystrophyPretreatment with Sodium Phenylbutyrate Alleviates Cerebral Ischemia/Reperfusion Injury by Upregulating DJ-1 Protein.Advancing host-directed therapy for tuberculosis.ABCD2 is a direct target of β-catenin and TCF-4: implications for X-linked adrenoleukodystrophy therapyThe Peroxisomal 3-keto-acyl-CoA thiolase B Gene Expression Is under the Dual Control of PPARα and HNF4α in the LiverPeroxisomal dysfunction in inflammatory childhood white matter disorders: an unexpected contributor to neuropathologyHistone deacetylase inhibitor upregulates peroxisomal fatty acid oxidation and inhibits apoptotic cell death in abcd1-deficient glial cells.HDAC inhibitor SAHA normalizes the levels of VLCFAs in human skin fibroblasts from X-ALD patients and downregulates the expression of proinflammatory cytokines in Abcd1/2-silenced mouse astrocytes.Mammalian peroxisomal ABC transporters: from endogenous substrates to pathology and clinical significance.Inside job: ligand-receptor pharmacology beneath the plasma membrane.Novel approaches to the treatment of sickle cell disease: the potential of histone deacetylase inhibitors.A Thyroid Hormone-Based Strategy for Correcting the Biochemical Abnormality in X-Linked Adrenoleukodystrophy.Phenylbutyrate up-regulates the DJ-1 protein and protects neurons in cell culture and in animal models of Parkinson disease.Immortalized keratinocytes derived from patients with epidermolytic ichthyosis reproduce the disease phenotype: a useful in vitro model for testing new treatments.Reduced expression of ATP7B affected by Wilson disease-causing mutations is rescued by pharmacological folding chaperones 4-phenylbutyrate and curcumin.High content screening for non-classical peroxisome proliferators.Functional rescue of mutant ABCA1 proteins by sodium 4-phenylbutyrate.Decrease of hepatic stellate cells in rats with enhanced sensitivity to clofibrate-induced hepatocarcinogenesis.Valproic acid induces antioxidant effects in X-linked adrenoleukodystrophy.Metformin-induced mitochondrial function and ABCD2 up-regulation in X-linked adrenoleukodystrophy involves AMP-activated protein kinase.
P2860
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P2860
Phenylbutyrate up-regulates the adrenoleukodystrophy-related gene as a nonclassical peroxisome proliferator
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2005 nî lūn-bûn
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2005年の論文
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2005年学术文章
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2005年学术文章
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name
Phenylbutyrate up-regulates th ...... ssical peroxisome proliferator
@ast
Phenylbutyrate up-regulates th ...... ssical peroxisome proliferator
@en
type
label
Phenylbutyrate up-regulates th ...... ssical peroxisome proliferator
@ast
Phenylbutyrate up-regulates th ...... ssical peroxisome proliferator
@en
prefLabel
Phenylbutyrate up-regulates th ...... ssical peroxisome proliferator
@ast
Phenylbutyrate up-regulates th ...... ssical peroxisome proliferator
@en
P2093
P2860
P50
P356
P1476
Phenylbutyrate up-regulates th ...... ssical peroxisome proliferator
@en
P2093
Alain Beley
Catherine Gondcaille
Dirk De Craemer
Frank Roels
Françoise Cadepond
Maria Rita Lecca
Marianne Depreter
Martine ElEtr
Maurice Bugaut
Nathalie Bertrand
P2860
P304
P356
10.1083/JCB.200501036
P407
P577
2005-04-04T00:00:00Z