about
Oxidative stress, mitochondrial and proteostasis malfunction in adrenoleukodystrophy: A paradigm for axonal degenerationImprovement of the Rett syndrome phenotype in a MeCP2 mouse model upon treatment with levodopa and a dopa-decarboxylase inhibitorABCD2 alters peroxisome proliferator-activated receptor α signaling in vitro, but does not impair responses to fenofibrate therapy in a mouse model of diet-induced obesityThe evolutionary origin of peroxisomes: an ER-peroxisome connection.Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy.Autophagy induction halts axonal degeneration in a mouse model of X-adrenoleukodystrophy.Oxidative damage compromises energy metabolism in the axonal degeneration mouse model of X-adrenoleukodystrophy.PeroxisomeDB: a database for the peroxisomal proteome, functional genomics and disease.Functional genomic analysis unravels a metabolic-inflammatory interplay in adrenoleukodystrophyPioglitazone halts axonal degeneration in a mouse model of X-linked adrenoleukodystrophyActivation of sirtuin 1 as therapy for the peroxisomal disease adrenoleukodystrophy.Phenylbutyrate up-regulates the adrenoleukodystrophy-related gene as a nonclassical peroxisome proliferatorOxidative stress modulates mitochondrial failure and cyclophilin D function in X-linked adrenoleukodystrophyTauroursodeoxycholic bile acid arrests axonal degeneration by inhibiting the unfolded protein response in X-linked adrenoleukodystrophy.Mitochondrial dysfunction and oxidative damage cooperatively fuel axonal degeneration in X-linked adrenoleukodystrophy.A key role for the peroxisomal ABCD2 transporter in fatty acid homeostasis.Valproic acid induces antioxidant effects in X-linked adrenoleukodystrophy.Oxidative stress regulates the ubiquitin-proteasome system and immunoproteasome functioning in a mouse model of X-adrenoleukodystrophy.Thyroid hormone induction of the adrenoleukodystrophy-related gene (ABCD2).Loss of SIRT2 leads to axonal degeneration and locomotor disability associated with redox and energy imbalance.Oxidative stress and mitochondrial dynamics malfunction are linked in Pelizaeus-Merzbacher disease.Impaired mitochondrial oxidative phosphorylation in the peroxisomal disease X-linked adrenoleukodystrophy.Steroid hormones control circadian Elovl3 expression in mouse liver.Epigenomic signature of adrenoleukodystrophy predicts compromised oligodendrocyte differentiation.Inhibition of Gsk3b Reduces Nfkb1 Signaling and Rescues Synaptic Activity to Improve the Rett Syndrome Phenotype in Mecp2-Knockout Mice.Aberrant regulation of the GSK-3β/NRF2 axis unveils a novel therapy for adrenoleukodystrophyLoss of the sphingolipid desaturase DEGS1 causes hypomyelinating leukodystrophyHigh-dose biotin restores redox balance, energy and lipid homeostasis, and axonal health in a model of adrenoleukodystrophy
P50
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P50
description
researcher
@en
wetenschapper
@nl
հետազոտող
@hy
name
Stéphane Fourcade
@ast
Stéphane Fourcade
@en
Stéphane Fourcade
@es
Stéphane Fourcade
@nl
type
label
Stéphane Fourcade
@ast
Stéphane Fourcade
@en
Stéphane Fourcade
@es
Stéphane Fourcade
@nl
prefLabel
Stéphane Fourcade
@ast
Stéphane Fourcade
@en
Stéphane Fourcade
@es
Stéphane Fourcade
@nl
P1053
N-4508-2014
P106
P31
P496
0000-0002-8031-5007