Liver disease in alpha-1 antitrypsin deficiency: current understanding and future therapy. - Wikidata - wikimedia - TriplyDB

Liver disease in alpha-1 antitrypsin deficiency: current understanding and future therapy.

Liver disease in alpha-1 antitrypsin deficiency: current understanding and future therapy.

http://www.wikidata.org/entity/Q38092867

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Liver tumors in children with metabolic disorders Challenges and Prospects for Alpha-1 Antitrypsin Deficiency Gene Therapy Alpha-1 antitrypsin Pi*SZ genotype: estimated prevalence and number of SZ subjects worldwide.Z α1-antitrypsin confers a proinflammatory phenotype that contributes to chronic obstructive pulmonary disease α1 Antitrypsin deficiency: current best practice in testing and augmentation therapy.A Library of Rare α1-Antitrypsin (AAT) Variant Phenotypes to Aid in the Diagnosis of AAT Deficiency.Gene Therapy for Alpha-1 Antitrypsin Deficiency Lung Disease.Liver Involvement in Patients With PiZZ-Emphysema, Candidates for Lung Transplantation.Using antisense technology to develop a novel therapy for α-1 antitrypsin deficient (AATD) liver disease and to model AATD lung disease.Measuring the Effect of Histone Deacetylase Inhibitors (HDACi) on the Secretion and Activity of Alpha-1 Antitrypsin.Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia.Pathophysiology of Alpha-1 Antitrypsin Deficiency Liver Disease.

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Liver disease in alpha-1 antitrypsin deficiency: current understanding and future therapy.

http://www.wikidata.org/entity/Q38092867

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Liver disease in alpha-1 antit ...... erstanding and future therapy.

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Liver disease in alpha-1 antit ...... erstanding and future therapy.

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Liver disease in alpha-1 antit ...... erstanding and future therapy.

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15412555.2013.765839

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COPD: Journal of Chronic Obstructive Pulmonary Disease

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Liver disease in alpha-1 antit ...... erstanding and future therapy.

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P2860

Grp78, Grp94, and Grp170 interact with alpha1-antitrypsin mutants that are retained in the endoplasmic reticulum

Alpha1-antitrypsin polymerization and the serpinopathies: pathobiology and prospects for therapy

Elucidation of the molecular logic by which misfolded alpha 1-antitrypsin is preferentially selected for degradation.

Organizational diversity among distinct glycoprotein endoplasmic reticulum-associated degradation programs

Alpha-1-antitrypsin deficiency: a new paradigm for hepatocellular carcinoma in genetic liver disease.

The mechanism of Z alpha 1-antitrypsin accumulation in the liver.

Respiratory symptoms and lung function in young adults with severe alpha(1)-antitrypsin deficiency (PiZZ)

A lag in intracellular degradation of mutant alpha 1-antitrypsin correlates with the liver disease phenotype in homozygous PiZZ alpha 1-antitrypsin deficiency.

Alpha-1-antitrypsin deficiency: diagnosis and treatment.

Rapamycin reduces intrahepatic alpha-1-antitrypsin mutant Z protein polymers and liver injury in a mouse model

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Jeffrey Teckman

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