Reactive oxygen species, oxidative stress, and cell death correlate with level of CoQ10 deficiency. - Wikidata - awgldk - TriplyDB

Reactive oxygen species, oxidative stress, and cell death correlate with level of CoQ10 deficiency.

Reactive oxygen species, oxidative stress, and cell death correlate with level of CoQ10 deficiency.

http://www.wikidata.org/entity/Q34378808

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The COQ2 genotype predicts the severity of coenzyme Q10 deficiency Dihydro-orotate dehydrogenase is physically associated with the respiratory complex and its loss leads to mitochondrial dysfunction Treatment of CoQ(10) deficient fibroblasts with ubiquinone, CoQ analogs, and vitamin C: time- and compound-dependent effects Dysfunctional Coq9 protein causes predominant encephalomyopathy associated with CoQ deficiency A defect in the mitochondrial complex III, but not complex IV, triggers early ROS-dependent damage in defined brain regions.CoQ10 Deficiency May Indicate Mitochondrial Dysfunction in Cr(VI) Toxicity.Mitochondrial dysfunction in inherited renal disease and acute kidney injury Pathomechanisms in coenzyme q10-deficient human fibroblasts.Effects of inhibiting CoQ10 biosynthesis with 4-nitrobenzoate in human fibroblasts.Membrane-bound CYB5R3 is a common effector of nutritional and oxidative stress response through FOXO3a and Nrf2.Renal mitochondrial cytopathies.176th ENMC International Workshop: diagnosis and treatment of coenzyme Q₁₀ deficiency Association of the COQ2 V393A Variant with Parkinson's Disease: A Case-Control Study and Meta-Analysis OTC Antioxidant Products for the Treatment of Cardiovascular and other Disorders: Popular Myth or Fact?Reduced coenzyme Q(10) in female smokers and its association with lipid profile in a young healthy adult population.CoQ(10) deficiencies and MNGIE: two treatable mitochondrial disorders.Lack of aprataxin impairs mitochondrial functions via downregulation of the APE1/NRF1/NRF2 pathway.Coenzyme Q10 restores oocyte mitochondrial function and fertility during reproductive aging Gene Therapy Corrects Mitochondrial Dysfunction in Hematopoietic Progenitor Cells and Fibroblasts from Coq9R239X Mice.Protecting the BBB endothelium against cigarette smoke-induced oxidative stress using popular antioxidants: Are they really beneficial?The submitochondrial distribution of ubiquinone affects respiration in long-lived Mclk1+/- mice Coenzyme Q10 defects may be associated with a deficiency of Q10-independent mitochondrial respiratory chain complexes.Mitochondrial function and lifespan of mice with controlled ubiquinone biosynthesis Tissue-specific oxidative stress and loss of mitochondria in CoQ-deficient Pdss2 mutant mice.Decreased Coenzyme Q10 Levels in Multiple System Atrophy Cerebellum Inhibition of oxidative stress by coenzyme Q10 increases mitochondrial mass and improves bioenergetic function in optic nerve head astrocytes.Synthesis and neuroprotective action of xyloketal derivatives in Parkinson's disease models.Coenzyme Q deficiency causes impairment of the sulfide oxidation pathway.CoQ deficiency causes disruption of mitochondrial sulfide oxidation, a new pathomechanism associated with this syndrome.Lipid dysfunction and pathogenesis of multiple system atrophy.Human mitochondrial DNA: roles of inherited and somatic mutations.Haploinsufficiency of COQ4 causes coenzyme Q10 deficiency.Coenzyme Q and mitochondrial disease Primary and secondary CoQ(10) deficiencies in humans.Molecular genetics of ubiquinone biosynthesis in animals.Genetic bases and clinical manifestations of coenzyme Q10 (CoQ 10) deficiency.Mutations in COQ4, an essential component of coenzyme Q biosynthesis, cause lethal neonatal mitochondrial encephalomyopathy.Indium chloride-induced micronuclei via reactive oxygen species in Chinese hamster lung fibroblast V79 cells.The Value of Coenzyme Q10 Determination in Mitochondrial Patients.Human neuronal coenzyme Q10 deficiency results in global loss of mitochondrial respiratory chain activity, increased mitochondrial oxidative stress and reversal of ATP synthase activity: implications for pathogenesis and treatment.

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P2860

Reactive oxygen species, oxidative stress, and cell death correlate with level of CoQ10 deficiency.

http://www.wikidata.org/entity/Q34378808

description

2010 nî lūn-bûn

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2010 թուականի Մայիսին հրատարակուած գիտական յօդուած

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2010 թվականի մայիսին հրատարակված գիտական հոդված

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2010年の論文

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2010年論文

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2010年論文

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2010年論文

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2010年論文

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2010年論文

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2010年论文

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Reactive oxygen species, oxida ...... ith level of CoQ10 deficiency.

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Reactive oxygen species, oxida ...... ith level of CoQ10 deficiency.

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Reactive oxygen species, oxida ...... ith level of CoQ10 deficiency.

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Reactive oxygen species, oxida ...... ith level of CoQ10 deficiency.

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Reactive oxygen species, oxida ...... ith level of CoQ10 deficiency.

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Reactive oxygen species, oxida ...... ith level of CoQ10 deficiency.

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Reactive oxygen species, oxida ...... ith level of CoQ10 deficiency.

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Reactive oxygen species, oxida ...... ith level of CoQ10 deficiency.

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Reactive oxygen species, oxida ...... ith level of CoQ10 deficiency.

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Ali B Naini

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Beatriz Dorado

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Catarina M Quinzii

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Filippo Santorelli

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Jorida Coku

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Leonardo Salviati

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Luis C López

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Markus Schuelke

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Meriem Tazir

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Michel Koenig

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P2860

A mutation in para-hydroxybenzoate-polyprenyl transferase (COQ2) causes primary coenzyme Q10 deficiency

A nonsense mutation in COQ9 causes autosomal-recessive neonatal-onset primary coenzyme Q10 deficiency: a potentially treatable form of mitochondrial disease

ADCK3, an ancestral kinase, is mutated in a form of recessive ataxia associated with coenzyme Q10 deficiency

COQ9, a new gene required for the biosynthesis of coenzyme Q in Saccharomyces cerevisiae.

Ubiquinone biosynthesis in Saccharomyces cerevisiae: the molecular organization of O-methylase Coq3p depends on Abc1p/Coq8p.

Missense mutation of the COQ2 gene causes defects of bioenergetics and de novo pyrimidine synthesis

Mitochondria and apoptosis

Mitochondrial control of cell death

Primary coenzyme Q deficiency in Pdss2 mutant mice causes isolated renal disease

Mechanism of neurodegeneration of neurons with mitochondrial DNA mutations.

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3733-3743

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10.1096/FJ.09-152728

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10

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24

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Salvatore DiMauro

Clotilde Lagier-Tourenne

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2010-05-21T00:00:00Z

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44623315

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20495179

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2996902

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