Aberrant CFTR-dependent HCO3- transport in mutations associated with cystic fibrosis.
about
Cystic Fibrosis: Lessons from the Sweat GlandMissense mutations in a retinal pigment epithelium protein, bestrophin-1, cause retinitis pigmentosaThe relevance of sweat testing for the diagnosis of cystic fibrosis in the genomic era.Acute regulation of the SLC26A3 congenital chloride diarrhoea anion exchanger (DRA) expressed in Xenopus oocytesPatterns of GI disease in adulthood associated with mutations in the CFTR geneAre p.I148T, p.R74W and p.D1270N cystic fibrosis causing mutations?Potential genetic modifiers of the cystic fibrosis intestinal inflammatory phenotype on mouse chromosomes 1, 9, and 10Neutrophil elastase and matrix metalloproteinase 12 in cystic fibrosis lung diseaseMolecular mechanism of pancreatic and salivary gland fluid and HCO3 secretionCFTR in cystic fibrosis and cholera: from membrane transport to clinical practiceIRBIT coordinates epithelial fluid and HCO3- secretion by stimulating the transporters pNBC1 and CFTR in the murine pancreatic ductSLC26A7 is a Cl- channel regulated by intracellular pHPolarized expression and function of P2Y ATP receptors in rat bile duct epitheliaMolecular characterization of the murine Slc26a6 anion exchanger: functional comparison with Slc26a1Dynamic control of cystic fibrosis transmembrane conductance regulator Cl(-)/HCO3(-) selectivity by external Cl(-)Lung infections associated with cystic fibrosis.Bicarbonate and functional CFTR channel are required for proper mucin secretion and link cystic fibrosis with its mucus phenotype.Cystic fibrosis transmembrane conductance regulator (CFTR) gene mutations and risk for pancreatic adenocarcinoma.A host defense mechanism involving CFTR-mediated bicarbonate secretion in bacterial prostatitis.Native small airways secrete bicarbonate.Stabilizing rescued surface-localized δf508 CFTR by potentiation of its interaction with Na(+)/H(+) exchanger regulatory factor 1.Inhibition of acinar apoptosis occurs during acute pancreatitis in the human homologue DeltaF508 cystic fibrosis mouse.A molecular mechanism for aberrant CFTR-dependent HCO(3)(-) transport in cystic fibrosis.A new role for bicarbonate in mucus formation.CFTR chloride channel in the apical compartments: spatiotemporal coupling to its interacting partners.CFTR mutations and polymorphisms in male infertility.Renal vacuolar H+-ATPase.Identification of uterine ion transporters for mineralisation precursors of the avian eggshellElectrolyte transport in the mammalian colon: mechanisms and implications for disease.Regulation of endogenous ENaC functional expression by CFTR and ΔF508-CFTR in airway epithelial cells.Towards the pharmacogenomics of cystic fibrosis.Embryonic frog epidermis: a model for the study of cell-cell interactions in the development of mucociliary disease.Corticosteroids correct aberrant CFTR localization in the duct and regenerate acinar cells in autoimmune pancreatitis.Functional anatomy of normal bile ducts.Insights into the molecular mechanisms of bradycardia-triggered arrhythmias in long QT-3 syndromeStructural determinants and significance of regulation of electrogenic Na(+)-HCO(3)(-) cotransporter stoichiometry.Chloride channels in the kidney: lessons learned from knockout animals.CFTR and bicarbonate secretion by [correction of to] epithelial cells.Slc26a6 regulates CFTR activity in vivo to determine pancreatic duct HCO3- secretion: relevance to cystic fibrosisAnimal models of gastrointestinal and liver diseases. Animal models of cystic fibrosis: gastrointestinal, pancreatic, and hepatobiliary disease and pathophysiology.
P2860
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P2860
Aberrant CFTR-dependent HCO3- transport in mutations associated with cystic fibrosis.
description
2001 nî lūn-bûn
@nan
2001年の論文
@ja
2001年論文
@yue
2001年論文
@zh-hant
2001年論文
@zh-hk
2001年論文
@zh-mo
2001年論文
@zh-tw
2001年论文
@wuu
2001年论文
@zh
2001年论文
@zh-cn
name
Aberrant CFTR-dependent HCO3- transport in mutations associated with cystic fibrosis.
@en
type
label
Aberrant CFTR-dependent HCO3- transport in mutations associated with cystic fibrosis.
@en
prefLabel
Aberrant CFTR-dependent HCO3- transport in mutations associated with cystic fibrosis.
@en
P2093
P2860
P356
P1433
P1476
Aberrant CFTR-dependent HCO3- transport in mutations associated with cystic fibrosis.
@en
P2093
P2860
P2888
P356
10.1038/35065099
P407
P50
P577
2001-03-01T00:00:00Z
P6179
1036809939