Defects in cholangiocyte fibrocystin expression and ciliary structure in the PCK rat. - Wikidata - awgldk - TriplyDB

Defects in cholangiocyte fibrocystin expression and ciliary structure in the PCK rat.

Defects in cholangiocyte fibrocystin expression and ciliary structure in the PCK rat.

http://www.wikidata.org/entity/Q52552433

about

PKHD1 protein encoded by the gene for autosomal recessive polycystic kidney disease associates with basal bodies and primary cilia in renal epithelial cells Polycystic kidney disease protein fibrocystin localizes to the mitotic spindle and regulates spindle bipolarity Ciliary and centrosomal defects associated with mutation and depletion of the Meckel syndrome genes MKS1 and MKS3 A polycystin-centric view of cyst formation and disease: the polycystins revisited ARPKD and early manifestations of ADPKD: the original polycystic kidney disease and phenocopies Polycystic liver diseases: advanced insights into the molecular mechanisms Physiology of cholangiocytes HDAC6 is overexpressed in cystic cholangiocytes and its inhibition reduces cystogenesis Cholangiocyte primary cilia are chemosensory organelles that detect biliary nucleotides via P2Y12 purinergic receptors Activation of the MEK5/ERK5 cascade is responsible for biliary dysgenesis in a rat model of Caroli's disease Cholangiocyte cilia detect changes in luminal fluid flow and transmit them into intracellular Ca2+ and cAMP signaling Inhibition of Pkhd1 impairs tubulomorphogenesis of cultured IMCD cells.Fibrocystin/polyductin modulates renal tubular formation by regulating polycystin-2 expression and function Pkd1 transgenic mice: adult model of polycystic kidney disease with extrarenal and renal phenotypes.Polyductin undergoes notch-like processing and regulated release from primary cilia Flagellar length control system: testing a simple model based on intraflagellar transport and turnover Polycystic kidney disease.Structural and functional analyses of liver cysts from the BALB/c-cpk mouse model of polycystic kidney disease Heterogeneity of the intrahepatic biliary epithelium Polycystic liver diseases.Activation of Trpv4 reduces the hyperproliferative phenotype of cystic cholangiocytes from an animal model of ARPKD.Novel Mutation in the PKHD1 Gene Diagnosed Prenatally in a Fetus with Autosomal Recessive Polycystic Kidney Disease.An incredible decade for the primary cilium: a look at a once-forgotten organelle.Aberrant glycosylation and localization of polycystin-1 cause polycystic kidney in an AQP11 knockout model.The cAMP effectors Epac and protein kinase a (PKA) are involved in the hepatic cystogenesis of an animal model of autosomal recessive polycystic kidney disease (ARPKD).Functional anatomy of normal bile ducts.Disease stage characterization of hepatorenal fibrocystic pathology in the PCK rat model of ARPKD Patients, cells, and organelles: the intersection of science and serendipity.The role of cilia in the regulation of bile flow.Deciphering physiological role of the mechanosensitive TRPV4 channel in the distal nephron.Biliary dysgenesis in the PCK rat, an orthologous model of autosomal recessive polycystic kidney disease Congenital hepatic fibrosis in autosomal recessive polycystic kidney disease.Polycystic diseases in visceral organs.Fibrocystin/polyductin, found in the same protein complex with polycystin-2, regulates calcium responses in kidney epithelia.Cholangiocytes with mesenchymal features contribute to progressive hepatic fibrosis of the polycystic kidney rat Cholangiocyte cilia express TRPV4 and detect changes in luminal tonicity inducing bicarbonate secretion.Functional polycystin-1 dosage governs autosomal dominant polycystic kidney disease severity.Diagnosis, pathogenesis, and treatment prospects in cystic kidney disease.Cholangiocyte anion exchange and biliary bicarbonate excretion Morphological and functional features of hepatic cyst epithelium in autosomal dominant polycystic kidney disease.

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P2860

Defects in cholangiocyte fibrocystin expression and ciliary structure in the PCK rat.

http://www.wikidata.org/entity/Q52552433

description

2003 nî lūn-bûn

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2003年の論文

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2003年学术文章

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2003年学术文章

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2003年学术文章

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2003年学术文章

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2003年学术文章

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2003年学术文章

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2003年學術文章

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2003年學術文章

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name

Defects in cholangiocyte fibrocystin expression and ciliary structure in the PCK rat.

@en

Defects in cholangiocyte fibrocystin expression and ciliary structure in the PCK rat.

@nl

type

label

Defects in cholangiocyte fibrocystin expression and ciliary structure in the PCK rat.

@en

Defects in cholangiocyte fibrocystin expression and ciliary structure in the PCK rat.

@nl

prefLabel

Defects in cholangiocyte fibrocystin expression and ciliary structure in the PCK rat.

@en

Defects in cholangiocyte fibrocystin expression and ciliary structure in the PCK rat.

@nl

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J.GASTRO.2003.09.001

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Defects in cholangiocyte fibrocystin expression and ciliary structure in the PCK rat.

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Anatoliy I Masyuk

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Bing Q Huang

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Christopher J Ward

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David Yuan

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Eric L Ritman

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Nicholas F LaRusso

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Patrick L Splinter

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Peter C Harris

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Rachaneekorn Punyashthiti

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Tatyana V Masyuk

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