Connexin30 deficiency causes instrastrial fluid-blood barrier disruption within the cochlear stria vascularis.
about
Gap junction mediated intercellular metabolite transfer in the cochlea is compromised in connexin30 null miceIdentification and characterization of pannexin expression in the mammalian cochleaThe endocochlear potential depends on two K+ diffusion potentials and an electrical barrier in the stria vascularis of the inner earHuman adenylate kinase 2 deficiency causes a profound hematopoietic defect associated with sensorineural deafnessEarly development of the vertebrate inner earFolic acid deficiency induces premature hearing loss through mechanisms involving cochlear oxidative stress and impairment of homocysteine metabolismNa+/K+-ATPase α1 identified as an abundant protein in the blood-labyrinth barrier that plays an essential role in the barrier integrityThe unique electrical properties in an extracellular fluid of the mammalian cochlea; their functional roles, homeostatic processes, and pathological significance.Coordinated control of connexin 26 and connexin 30 at the regulatory and functional level in the inner earThe human deafness-associated connexin 30 T5M mutation causes mild hearing loss and reduces biochemical coupling among cochlear non-sensory cells in knock-in mice.A connexin30 mutation rescues hearing and reveals roles for gap junctions in cochlear amplification and micromechanicsOrgan of Corti and Stria Vascularis: Is there an Interdependence for Survival?Immunohistochemical localization of OCT2 in the cochlea of various species.Structural changes in thestrial blood-labyrinth barrier of aged C57BL/6 mice.Potassium ion movement in the inner ear: insights from genetic disease and mouse modelsLipopolysaccharide-induced middle ear inflammation disrupts the cochlear intra-strial fluid-blood barrier through down-regulation of tight junction proteins.Genetics of auditory mechano-electrical transduction.Perivascular macrophage-like melanocyte responsiveness to acoustic trauma--a salient feature of strial barrier associated hearing loss.Feline deafness.Endothelial cell, pericyte, and perivascular resident macrophage-type melanocyte interactions regulate cochlear intrastrial fluid-blood barrier permeabilityPhysiopathology of the cochlear microcirculationCalcium signaling in the cochlea - Molecular mechanisms and physiopathological implications.Perivascular-resident macrophage-like melanocytes in the inner ear are essential for the integrity of the intrastrial fluid-blood barrier.BAAV mediated GJB2 gene transfer restores gap junction coupling in cochlear organotypic cultures from deaf Cx26Sox10Cre mice.Advances in Auditory and Vestibular Medicine.Gap-junction channels dysfunction in deafness and hearing loss.ATP-mediated cell-cell signaling in the organ of Corti: the role of connexin channels.Cochlear Homocysteine Metabolism at the Crossroad of Nutrition and Sensorineural Hearing Loss.Matrix imbalance by inducing expression of metalloproteinase and oxidative stress in cochlea of hyperhomocysteinemic mice.Gap junctions and blood-tissue barriersCompetitive antagonism of fluorescent gentamicin uptake in the cochleaThe role of gap junction channels during physiologic and pathologic conditions of the human central nervous systemSerum homocysteine and folate concentrations are associated with prevalent age-related hearing loss.Spinster homolog 2 (spns2) deficiency causes early onset progressive hearing loss.Molecular architecture of the stria vascularis membrane transport system, which is essential for physiological functions of the mammalian cochlea.Deletion of astroglial connexins weakens the blood-brain barrier.Folic acid improves inner ear vascularization in hyperhomocysteinemic miceStrial microvascular pathology and age-associated endocochlear potential decline in NOD congenic mice.Isolation and culture of endothelial cells, pericytes and perivascular resident macrophage-like melanocytes from the young mouse ear.Cx36 makes channels coupling human pancreatic beta-cells, and correlates with insulin expression.
P2860
Q21092155-400F2BAE-84EA-4B7C-A301-D4403F0A970FQ24646253-766CB5B3-3597-4B6E-998E-887FD1FDD364Q24652355-8BC94FCC-5214-427C-92CA-96B1EA22C388Q24655619-5B097188-E962-4D97-BB7D-543126D85060Q26823188-4E3D5CBD-2C69-44FC-AD46-167B408FB675Q27319467-12F28846-4E4E-40A8-A42D-4E66413D5948Q27437624-4D56E521-0D24-4687-B7B7-8F886141A39FQ28076301-1171F78B-A1E8-4C0B-A259-20F04771A3ABQ28302365-12AD3E4C-E1A0-4160-977C-01F293E51F46Q28748215-2E5D1B38-97A3-415C-966D-E3461AA6D70CQ30362375-C308EBE4-EDE3-4F60-9055-AE6C1113CC8CQ30365442-71F12D75-54CF-4F3A-BBFE-A6EDE7E511AAQ30368484-607E8431-0741-4085-977A-7C2665878CA4Q30375115-9A3C3B0D-3729-40F4-B82A-7149F32B19A4Q30413390-2B387214-56F8-4FCC-8382-22A376899BEBQ30414927-C4DD1EBF-2A5C-421D-95EB-DB4EB1207BFBQ30421422-09D77B76-0117-495B-9DCF-6E4F50BE28ADQ30431803-33846D74-D7E5-4E8E-8A9F-D9C7A5370480Q30447868-827582EC-8066-44A1-9669-D4ED33EF3F97Q30454432-0A36C1EE-907A-49ED-BD0F-A4AAB81C4A3BQ30456047-1B98EDE4-347F-4253-923A-04740F0F4212Q30465350-278DFC2B-3109-470C-9341-55383540F624Q30465922-585B6E73-C40A-4400-88E0-9D9777106104Q30474429-9A7DFCCF-F6AA-4509-B40B-CF9B10287AA9Q30480012-F734D9B0-DA68-4829-BAA5-38763F0992D8Q30490087-43F33F61-B119-4AC9-9299-60E365BD2A62Q30495800-24041049-B024-4A0B-A5EA-8CEBD5088EE2Q33600227-0A489277-0CB9-4B22-AE85-B69C8F06F023Q33824379-2446F7F4-CE49-4D0B-8004-44DBE4E8B7D1Q33941978-565F533C-66A7-40FF-A642-31AA6FC0F903Q34071857-DD48527A-F25A-4920-ADC3-F9A9D1B830E5Q34262821-FC9E1091-CA6C-4E16-86C2-F3918A5C3468Q34620917-435EB190-2D69-4A93-B260-6144BD819BA4Q35377676-E1958AFE-0696-4413-B7F1-4C1286A02D65Q35659340-8B1395A6-A632-4A3D-BC89-FCD81FCF822DQ36170335-468E744B-84F8-4F6F-8A1B-6E98981FE932Q36720069-D4BCB1F7-3A3F-45ED-91FA-EF3010E275D1Q37071828-06E4A9DB-3D5C-4985-867A-C45A609A8016Q37088047-004BA788-04A0-4C3A-9E59-EC4E71FD2C58Q37090060-B2A14666-3399-4922-8F7C-45360E529D01
P2860
Connexin30 deficiency causes instrastrial fluid-blood barrier disruption within the cochlear stria vascularis.
description
2007 nî lūn-bûn
@nan
2007 թուականի Մարտին հրատարակուած գիտական յօդուած
@hyw
2007 թվականի մարտին հրատարակված գիտական հոդված
@hy
2007年の論文
@ja
2007年論文
@yue
2007年論文
@zh-hant
2007年論文
@zh-hk
2007年論文
@zh-mo
2007年論文
@zh-tw
2007年论文
@wuu
name
Connexin30 deficiency causes i ...... the cochlear stria vascularis.
@ast
Connexin30 deficiency causes i ...... the cochlear stria vascularis.
@en
type
label
Connexin30 deficiency causes i ...... the cochlear stria vascularis.
@ast
Connexin30 deficiency causes i ...... the cochlear stria vascularis.
@en
prefLabel
Connexin30 deficiency causes i ...... the cochlear stria vascularis.
@ast
Connexin30 deficiency causes i ...... the cochlear stria vascularis.
@en
P2093
P2860
P50
P356
P1476
Connexin30 deficiency causes i ...... the cochlear stria vascularis.
@en
P2093
Béatrice Regnault
Dorothée Caille
Karine Demuth
Nadège Cayet
Paolo Meda
P2860
P304
P356
10.1073/PNAS.0605108104
P407
P577
2007-03-30T00:00:00Z