Sudden death and cardiovascular collapse in children with restrictive cardiomyopathy.
about
Cardiac troponin mutations and restrictive cardiomyopathyIdiopathic restrictive cardiomyopathy is part of the clinical expression of cardiac troponin I mutationsA troponin T mutation that causes infantile restrictive cardiomyopathy increases Ca2+ sensitivity of force development and impairs the inhibitory properties of troponin2015 ESC Guidelines for the management of patients with ventricular arrhythmias and the prevention of sudden cardiac death: The Task Force for the Management of Patients with Ventricular Arrhythmias and the Prevention of Sudden Cardiac Death of theCardiac-myocyte-specific excision of the vinculin gene disrupts cellular junctions, causing sudden death or dilated cardiomyopathyCorrecting diastolic dysfunction by Ca2+ desensitizing troponin in a transgenic mouse model of restrictive cardiomyopathyPediatric heart transplantation-indications and outcomes in the current era.Ventricular septal defect and restrictive cardiomyopathy in a paediatric TNNI3 mutation carrier.Cardiomyopathy: an overviewThe impact of heart failure severity at time of listing for cardiac transplantation on survival in pediatric cardiomyopathy.Idiopathic restrictive cardiomyopathy in childrenAn unusual ECG pattern in restrictive cardimyopathyInsights into restrictive cardiomyopathy from clinical and animal studies.Cardiomyopathy With Restrictive Physiology in Sickle Cell DiseaseAllele and species dependent contractile defects by restrictive and hypertrophic cardiomyopathy-linked troponin I mutantsClinical Characteristics and Treatment of Cardiomyopathies in Children.Sudden unexpected death in children with heart disease.Impaired relaxation is the main manifestation in transgenic mice expressing a restrictive cardiomyopathy mutation, R193H, in cardiac TnI.Pediatric cardiomyopathies: causes, epidemiology, clinical course, preventive strategies and therapies.Clinical practice: heart failure in children. Part I: clinical evaluation, diagnostic testing, and initial medical management.The genetics of cardiomyopathy: genotyping and genetic counseling.Inherited cardiomyopathies caused by troponin mutations.Sex differences in cardiomyopathies.Applicability of published guidelines for assessment of left ventricular diastolic function in adults to children with restrictive cardiomyopathy: an observational study.Experimental models of inherited cardiomyopathy and its therapeutics.Hypercontractile mutant of ventricular myosin essential light chain leads to disruption of sarcomeric structure and function and results in restrictive cardiomyopathy in mice.Restrictive Cardiomyopathy Caused by Troponin Mutations: Application of Disease Animal Models in Translational StudiesA reappraisal of the mechanisms underlying the cardiac complications of sickle cell anemia.Intraoperative management of atrial fibrillation in a patient with restrictive cardiomyopathy.Dose-dependent diastolic dysfunction and early death in a mouse model with cardiac troponin mutations.Pathogenesis associated with a restrictive cardiomyopathy mutant in cardiac troponin T is due to reduced protein stability and greatly increased myofilament Ca2+ sensitivity.Mutations in human cardiac troponin I that are associated with restrictive cardiomyopathy affect basal ATPase activity and the calcium sensitivity of force development.Sudden death possibly related to lenalidomide given for cardiac and muscle AL amyloidosis secondary to light chain deposition disease.Acute Ischemic Pediatric Stroke Management: An Extended Window for Mechanical Thrombectomy?Rare Diagnosis in a 4-Year-Old Boy Presenting With Shortness of Breath.Cardiac transplantation in a pediatric patient with systemic sclerosis.Arrhythmic Burden and Ambulatory Monitoring of Pediatric Patients with Cardiomyopathy.Cardiomyopathy in Coffin-Lowry syndrome.
P2860
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P2860
Sudden death and cardiovascular collapse in children with restrictive cardiomyopathy.
description
2000 nî lūn-bûn
@nan
2000 թուականի Օգոստոսին հրատարակուած գիտական յօդուած
@hyw
2000 թվականի օգոստոսին հրատարակված գիտական հոդված
@hy
2000年の論文
@ja
2000年論文
@yue
2000年論文
@zh-hant
2000年論文
@zh-hk
2000年論文
@zh-mo
2000年論文
@zh-tw
2000年论文
@wuu
name
Sudden death and cardiovascular collapse in children with restrictive cardiomyopathy.
@ast
Sudden death and cardiovascular collapse in children with restrictive cardiomyopathy.
@en
type
label
Sudden death and cardiovascular collapse in children with restrictive cardiomyopathy.
@ast
Sudden death and cardiovascular collapse in children with restrictive cardiomyopathy.
@en
prefLabel
Sudden death and cardiovascular collapse in children with restrictive cardiomyopathy.
@ast
Sudden death and cardiovascular collapse in children with restrictive cardiomyopathy.
@en
P2093
P356
P1433
P1476
Sudden death and cardiovascular collapse in children with restrictive cardiomyopathy.
@en
P2093
P304
P356
10.1161/01.CIR.102.8.876
P407
P577
2000-08-01T00:00:00Z