Long-term rescue of a familial hypertrophic cardiomyopathy caused by a mutation in the thin filament protein, tropomyosin, via modulation of a calcium cycling protein.
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Myosin binding protein C: implications for signal-transductionTropomyosin de-phosphorylation in the heart: what are the consequences?Desensitization of myofilaments to Ca2+ as a therapeutic target for hypertrophic cardiomyopathy with mutations in thin filament proteins.SERCA2 Haploinsufficiency in a Mouse Model of Darier Disease Causes a Selective Predisposition to Heart FailureIn Vivo Analysis of Troponin C Knock-In (A8V) Mice: Evidence that TNNC1 Is a Hypertrophic Cardiomyopathy Susceptibility GeneTropomyosin dephosphorylation results in compensated cardiac hypertrophyConserved Asp-137 is important for both structure and regulatory functions of cardiac α-tropomyosin (α-TM) in a novel transgenic mouse model expressing α-TM-D137LMicroarray analysis of active cardiac remodeling genes in a familial hypertrophic cardiomyopathy mouse model rescued by a phospholamban knockout.Decreasing tropomyosin phosphorylation rescues tropomyosin-induced familial hypertrophic cardiomyopathyp90 ribosomal S6 kinase 3 contributes to cardiac insufficiency in α-tropomyosin Glu180Gly transgenic micePredicting Effects of Tropomyosin Mutations on Cardiac Muscle Contraction through Myofilament Modeling.Early sensitization of myofilaments to Ca2+ prevents genetically linked dilated cardiomyopathy in mice.Therapeutic Strategies Targeting Inherited Cardiomyopathies.The allosteric glycogen synthase kinase-3 inhibitor NP12 limits myocardial remodeling and promotes angiogenesis in an acute myocardial infarction model.
P2860
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P2860
Long-term rescue of a familial hypertrophic cardiomyopathy caused by a mutation in the thin filament protein, tropomyosin, via modulation of a calcium cycling protein.
description
2011 nî lūn-bûn
@nan
2011年の論文
@ja
2011年論文
@yue
2011年論文
@zh-hant
2011年論文
@zh-hk
2011年論文
@zh-mo
2011年論文
@zh-tw
2011年论文
@wuu
2011年论文
@zh
2011年论文
@zh-cn
name
Long-term rescue of a familial ...... of a calcium cycling protein.
@ast
Long-term rescue of a familial ...... of a calcium cycling protein.
@en
type
label
Long-term rescue of a familial ...... of a calcium cycling protein.
@ast
Long-term rescue of a familial ...... of a calcium cycling protein.
@en
prefLabel
Long-term rescue of a familial ...... of a calcium cycling protein.
@ast
Long-term rescue of a familial ...... of a calcium cycling protein.
@en
P2093
P2860
P1476
Long-term rescue of a familial ...... of a calcium cycling protein.
@en
P2093
Beata M Wolska
David F Wieczorek
Evangelia G Kranias
Fernando A L Dias
James R Peña
Lynley S Heinrich
Marco S L Alves
Paul H Goldspink
Robert D Gaffin
Shamim A K Chowdhury
P2860
P304
P356
10.1016/J.YJMCC.2011.07.026
P577
2011-08-05T00:00:00Z