Two Small Molecules Restore Stability to a Subpopulation of the Cystic Fibrosis Transmembrane Conductance Regulator with the Predominant Disease-causing Mutation.
about
Correction of CFTR function in nasal epithelial cells from cystic fibrosis patients predicts improvement of respiratory function by CFTR modulators.Investigation of the effects of the CFTR potentiator ivacaftor on human P-glycoprotein (ABCB1).Partial rescue of F508del-CFTR channel gating with modest improvement of protein processing, but not stability by a dual-acting small molecule.NM23 proteins: innocent bystanders or local energy boosters for CFTR?CFTR potentiators: from bench to bedside.Dissection of the Role of VIMP in Endoplasmic Reticulum-Associated Degradation of CFTRΔF508.
P2860
Two Small Molecules Restore Stability to a Subpopulation of the Cystic Fibrosis Transmembrane Conductance Regulator with the Predominant Disease-causing Mutation.
description
2017 nî lūn-bûn
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2017年の論文
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2017年論文
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2017年論文
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2017年論文
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2017年論文
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2017年論文
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2017年论文
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2017年论文
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2017年论文
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name
Two Small Molecules Restore St ...... nant Disease-causing Mutation.
@en
type
label
Two Small Molecules Restore St ...... nant Disease-causing Mutation.
@en
prefLabel
Two Small Molecules Restore St ...... nant Disease-causing Mutation.
@en
P2093
P2860
P356
P1476
Two Small Molecules Restore St ...... inant Disease-causing Mutation
@en
P2093
David N Sheppard
Joe A Wrennall
Robert C Ford
Xiaomeng Wang
Yiting Wang
Zhiwei Cai
P2860
P304
P356
10.1074/JBC.M116.751537
P407
P577
2017-01-13T00:00:00Z