Role of low native state kinetic stability and interaction of partially unfolded states with molecular chaperones in the mitochondrial protein mistargeting associated with primary hyperoxaluria.
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Crystal structure of the S187F variant of human liver alanine: Aminotransferase associated with primary hyperoxaluria type I and its functional implicationsThe Role of Protein Denaturation Energetics and Molecular Chaperones in the Aggregation and Mistargeting of Mutants Causing Primary Hyperoxaluria Type IThe consensus-based approach for gene/enzyme replacement therapies and crystallization strategies: the case of human alanine-glyoxylate aminotransferaseProtein homeostasis disorders of key enzymes of amino acids metabolism: mutation-induced protein kinetic destabilization and new therapeutic strategies.S81L and G170R mutations causing Primary Hyperoxaluria type I in homozygosis and heterozygosis: an example of positive interallelic complementation.Irreversible denaturation of maltodextrin glucosidase studied by differential scanning calorimetry, circular dichroism, and turbidity measurementsAllele-specific characterization of alanine: glyoxylate aminotransferase variants associated with primary hyperoxaluriaThe peroxisomal protein import machinery displays a preference for monomeric substrates.Phenotype-Genotype Correlations and Estimated Carrier Frequencies of Primary Hyperoxaluria.An update on primary hyperoxaluria.Hyperoxaluria and systemic oxalosis: an update on current therapy and future directions.Protein homeostasis defects of alanine-glyoxylate aminotransferase: new therapeutic strategies in primary hyperoxaluria type I.Innovative strategies to treat protein misfolding in inborn errors of metabolism: pharmacological chaperones and proteostasis regulators.Protein Stability, Folding and Misfolding in Human PGK1 Deficiency.Molecular recognition of PTS-1 cargo proteins by Pex5p: implications for protein mistargeting in primary hyperoxaluria.Correlation between the molecular effects of mutations at the dimer interface of alanine-glyoxylate aminotransferase leading to primary hyperoxaluria type I and the cellular response to vitamin B6.Folding Defects Leading to Primary Hyperoxaluria.Oligomeric status of human cystathionine beta-synthase modulates AdoMet binding.Evolutionary Divergent Suppressor Mutations in Conformational Diseases
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P2860
Role of low native state kinetic stability and interaction of partially unfolded states with molecular chaperones in the mitochondrial protein mistargeting associated with primary hyperoxaluria.
description
2010 nî lūn-bûn
@nan
2010年の論文
@ja
2010年論文
@yue
2010年論文
@zh-hant
2010年論文
@zh-hk
2010年論文
@zh-mo
2010年論文
@zh-tw
2010年论文
@wuu
2010年论文
@zh
2010年论文
@zh-cn
name
Role of low native state kinet ...... ed with primary hyperoxaluria.
@en
Role of low native state kinet ...... ed with primary hyperoxaluria.
@nl
type
label
Role of low native state kinet ...... ed with primary hyperoxaluria.
@en
Role of low native state kinet ...... ed with primary hyperoxaluria.
@nl
prefLabel
Role of low native state kinet ...... ed with primary hyperoxaluria.
@en
Role of low native state kinet ...... ed with primary hyperoxaluria.
@nl
P2860
P1433
P1476
Role of low native state kinet ...... ted with primary hyperoxaluria
@en
P2093
Eduardo Salido
P2860
P2888
P304
P356
10.1007/S00726-010-0801-2
P577
2010-11-20T00:00:00Z