Adreno-leukodystrophy: oxidative stress of mice and men. - Wikidata - wikimedia - TriplyDB

Adreno-leukodystrophy: oxidative stress of mice and men.

Adreno-leukodystrophy: oxidative stress of mice and men.

http://www.wikidata.org/entity/Q46829099

about

The role of ELOVL1 in very long-chain fatty acid homeostasis and X-linked adrenoleukodystrophy Current and future pharmacological treatment strategies in X-linked adrenoleukodystrophy Peroxisomes in brain development and function X-linked adrenoleukodystrophy (X-ALD): clinical presentation and guidelines for diagnosis, follow-up and management.Deficiency of ferritin heavy-chain nuclear import in triple a syndrome implies nuclear oxidative damage as the primary disease mechanism Oxidative stress and adrenocortical insufficiency.Very long-chain fatty acid accumulation causes lipotoxic response via 5-lipoxygenase in cerebral adrenoleukodystrophy.Abcd2 is a strong modifier of the metabolic impairments in peritoneal macrophages of ABCD1-deficient mice No evidence for the reversal of adrenal failure after hematopoietic cell transplantation in X-linked adrenoleukodystrophy Pathophysiology of X-linked adrenoleukodystrophy.Pathomechanisms underlying X-adrenoleukodystrophy: a three-hit hypothesis.Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy.Peroxisomal dysfunction in inflammatory childhood white matter disorders: an unexpected contributor to neuropathology Autophagy induction halts axonal degeneration in a mouse model of X-adrenoleukodystrophy.ABCD1 deletion-induced mitochondrial dysfunction is corrected by SAHA: implication for adrenoleukodystrophy.Chitotriosidase as a biomarker of cerebral adrenoleukodystrophy Deletion of a single allele of the Pex11β gene is sufficient to cause oxidative stress, delayed differentiation and neuronal death in mouse brain Functional genomic analysis unravels a metabolic-inflammatory interplay in adrenoleukodystrophy Spinal cord trauma and the molecular point of no return Pioglitazone halts axonal degeneration in a mouse model of X-linked adrenoleukodystrophy Activation of sirtuin 1 as therapy for the peroxisomal disease adrenoleukodystrophy.Detection and Quantification of Free Radicals in Peroxisomal Disorders: A Comparative Study with Oxidative Stress Parameters The gene expression profiles of induced pluripotent stem cells from individuals with childhood cerebral adrenoleukodystrophy are consistent with proposed mechanisms of pathogenesis Neurodegeneration in a Drosophila model of adrenoleukodystrophy: the roles of the Bubblegum and Double bubble acyl-CoA synthetases.Plasmalogen deficiency in cerebral adrenoleukodystrophy and its modulation by lovastatin Silencing of Abcd1 and Abcd2 genes sensitizes astrocytes for inflammation: implication for X-adrenoleukodystrophy.Glutathione imbalance in patients with X-linked adrenoleukodystrophy The role of animal models in evaluating reasonable safety and efficacy for human trials of cell-based interventions for neurologic conditions Childhood Cerebral Adrenoleukodystrophy: MR Perfusion Measurements and Their Use in Predicting Clinical Outcome after Hematopoietic Stem Cell Transplantation.Oxidative imbalance in nonstimulated X-adrenoleukodystrophy-derived lymphoblasts Tauroursodeoxycholic bile acid arrests axonal degeneration by inhibiting the unfolded protein response in X-linked adrenoleukodystrophy.Myelin lesions associated with lysosomal and peroxisomal disorders.X-linked adrenoleukodystrophy: pathogenesis and treatment.Peroxisome-mitochondria interplay and disease.Oxidative Stress in Patients with X-Linked Adrenoleukodystrophy.X-linked adrenoleukodystrophy: very long-chain fatty acid metabolism is severely impaired in monocytes but not in lymphocytes.Intensity of MRI Gadolinium Enhancement in Cerebral Adrenoleukodystrophy: A Biomarker for Inflammation and Predictor of Outcome following Transplantation in Higher Risk Patients.Mechanisms of Antioxidant Induction with High-Dose N-Acetylcysteine in Childhood Cerebral Adrenoleukodystrophy.Evidence of Oxidative Stress and Secondary Mitochondrial Dysfunction in Metabolic and Non-Metabolic Disorders.Valproic acid induces antioxidant effects in X-linked adrenoleukodystrophy.

P2860

Q24300003-079AB656-BAAB-460F-A0FA-81F4F08DCFF8 Q24618949-216F88D9-9810-4B10-A076-8214FA8DA329 Q26774697-A99E2D30-418B-4C92-A4CB-1656F8F865B7 Q30460666-AC00DD3B-0F58-49CE-9BB6-A1F6F72A4D72 Q33512291-6FC83CC1-7595-44FD-A441-E907F38AD20C Q33709973-804EA195-6E8E-4F74-B0A0-C094FD6DDFDF Q33902055-F9FBBBDB-3841-41AA-8EEC-B35E32E22EAA Q34257373-0C4D4F20-EB77-401B-AA62-4035CDCADED1 Q34258459-C429F0C3-C45B-4FD5-A6FD-7020F48DF0EC Q34390414-69EFE946-E41B-48FE-B274-5BE77B5C0AAB Q34491978-1FD748BD-72A1-4112-BC72-9DD900873A54 Q34631169-E3AA34B8-B58F-4EA9-BCA1-FE43E4C02F81 Q34801173-2501377B-F6E5-473F-9040-CE97F8216689 Q35092638-265F963F-39CB-4E0A-8BD1-9C80FAEEC2F3 Q35417932-54374E99-9A08-4731-B5BC-9939CB8EE810 Q35607856-340B8222-8924-4DB5-BA20-AE5F63A343D9 Q35665063-F2E54A9F-79EE-49ED-ABF7-20CF5B418C80 Q35750216-363C8049-830F-438B-836C-D72C30F63E62 Q35822396-28E5A9A7-DC72-4F16-8157-F88AA7F31471 Q35997389-B2ED9C5F-1DD3-469F-BD92-FFFC5391EDF9 Q36288305-7F2A3AC5-BE72-4D2A-9F8C-40A61094EBCD Q36343707-E1948FE1-728A-4D55-AFF6-D54DF7356A9B Q36632900-8C41EB41-AC3B-468B-8D98-C1F2DD3ADC53 Q36856014-889F342A-C425-4A97-9AB1-94978A1DBC0F Q36953948-35C82728-DD02-4BEB-B4DB-8F8003719EFA Q37014934-7A60DED7-64D2-4AAB-AA56-C4CDE4BF8F7B Q37066947-6F0CB584-8E1E-4DB1-B293-ABB2A8A43DEE Q37193794-E511AD2A-2739-4812-97E8-BADFB1D90DA6 Q37246713-0B1FAB9E-20C7-4BFA-9091-97B7D78EE504 Q37347171-A8768EE4-CEFB-4297-990C-EFAF2F00C466 Q37596791-6196EE0F-5610-4311-8A39-7C2824A56F0C Q37785556-5A0C53BF-B89E-493F-B280-5275AAC21903 Q38239213-43B93E60-FD78-4983-A8D7-9270BC3DE087 Q38357539-4BCDAE43-0366-49A2-BAA9-4EDBB0D9A920 Q38546277-0AEA1AA8-F0AD-48C1-9FB6-16D4FE5813E1 Q38806290-FAE6902C-248B-4119-AAA7-BA6D3C70F085 Q39679149-FD1387C4-C851-4EF9-9FBF-1E5F54C4F1F9 Q40209375-227A1B98-4918-4057-8CFD-171323250FF4 Q41161393-598153D0-F91E-42BC-8F40-C9F9F6AD2970 Q43152628-7AE19F4D-C4FF-4B2F-9FCF-C86C77A67D7F

P2860

Adreno-leukodystrophy: oxidative stress of mice and men.

http://www.wikidata.org/entity/Q46829099

description

2005 nî lūn-bûn

@nan

2005年の論文

@ja

2005年学术文章

@wuu

2005年学术文章

@zh

2005年学术文章

@zh-cn

2005年学术文章

@zh-hans

2005年学术文章

@zh-my

2005年学术文章

@zh-sg

2005年學術文章

@yue

2005年學術文章

@zh-hant

name

Adreno-leukodystrophy: oxidative stress of mice and men.

@en

Adreno-leukodystrophy: oxidative stress of mice and men.

@nl

type

label

Adreno-leukodystrophy: oxidative stress of mice and men.

@en

Adreno-leukodystrophy: oxidative stress of mice and men.

@nl

prefLabel

Adreno-leukodystrophy: oxidative stress of mice and men.

@en

Adreno-leukodystrophy: oxidative stress of mice and men.

@nl

P1433

Q46829099-967D025F-0027-4EB3-993E-693C34A0B531

P1476

Q46829099-102318E4-0C2F-4164-92BD-1042E35014A6

P2093

Q46829099-36EEA3F0-A54D-4993-ADBF-52595DE3AF79

Q46829099-52DBFDCB-8613-4811-9F85-49D172FA0B48

Q46829099-5FB845B1-C61B-4A5F-B153-0EDACDD95FB5

Q46829099-630EBEBF-85C0-4C63-8F34-B3ECEE3926C4

Q46829099-C5772AA1-5678-4ECE-97EE-766E00FF7B5D

Q46829099-E465296F-7B8D-4ACE-9DF7-B25D69134B6B

Q46829099-E67D4C52-B383-4AAA-9632-1EDD252CA4FD

Q46829099-FEA52AC5-D259-4013-BA47-8EC542C4E177

P2860

Q46829099-1AD51E6D-675E-4896-8E21-3611FA6430BF

Q46829099-1CA9DD9A-56E0-4F0F-A13C-98D83F6F01BC

Q46829099-2D61C362-52EB-4CEB-915C-5FB1DA98CBB0

Q46829099-30B512B4-B61C-4A13-8FA6-D0C8A5984378

Q46829099-32A3152E-504A-438A-B1AB-8D6099155AE9

Q46829099-37248B07-453F-45F1-B6FD-1140C41F32B9

Q46829099-4893759F-6B81-41A8-A04D-77850B8D2B57

Q46829099-5171CE61-2465-43AD-ADB3-251A67D5F5E3

Q46829099-5719E775-A3AE-41F2-8C88-6EC66D9DB1FB

Q46829099-5B5B9353-6443-4F89-A406-39AF5CE5A6B6

P304

Q46829099-83D20594-D4E2-4B00-9E6E-8094ADD897B4

P31

Q46829099-9BC480DA-EEA3-496F-9AA9-6A10A1AB30CE

P356

Q46829099-3FA92A7C-DA27-4A14-B93C-011008E91F51

P433

Q46829099-A267D2B7-975A-433F-9B6D-E4E4F4709CD0

P478

Q46829099-BB04C1E5-4918-40C9-A531-BB4C45D0CE9E

P577

Q46829099-484D76D5-BC21-41CA-9662-EB7704E754FF

P698

Q46829099-D3E05526-486C-4F59-B2C1-AC2BD003F36F

P356

01.JNEN.0000190064.28559.A4

P1433

Journal of Neuropathology & Experimental Neurology

P1476

Adreno-leukodystrophy: oxidative stress of mice and men.

@en

P2093

Ann B Moser

http://www.w3.org/2001/XMLSchema#string

Ann K Heinzer

http://www.w3.org/2001/XMLSchema#string

Hugo W Moser

http://www.w3.org/2001/XMLSchema#string

James M Powers

http://www.w3.org/2001/XMLSchema#string

Kirby D Smith

http://www.w3.org/2001/XMLSchema#string

Paul A Watkins

http://www.w3.org/2001/XMLSchema#string

Rebecca Deering

http://www.w3.org/2001/XMLSchema#string

Zhengtong Pei

http://www.w3.org/2001/XMLSchema#string

P2860

Putative X-linked adrenoleukodystrophy gene shares unexpected homology with ABC transporters

Adrenoleukodystrophy: evidence for X linkage, inactivation, and selection favoring the mutant allele in heterozygous cells

Adrenoleukodystrophy protein-deficient mice represent abnormality of very long chain fatty acid metabolism

Chemistry and biochemistry of 4-hydroxynonenal, malonaldehyde and related aldehydes

The gene responsible for adrenoleukodystrophy encodes a peroxisomal membrane protein

Targeted inactivation of the X-linked adrenoleukodystrophy gene in mice.

Apoptosis and necrosis: two distinct events induced, respectively, by mild and intense insults with N-methyl-D-aspartate or nitric oxide/superoxide in cortical cell cultures.

Immune function of microglia.

Inducible nitric oxide synthase in T cells regulates T cell death and immune memory.

Immune function of astrocytes.

P304

1067-1079

http://www.w3.org/2001/XMLSchema#string

P31

scholarly article

P356

10.1097/01.JNEN.0000190064.28559.A4

http://www.w3.org/2001/XMLSchema#string

P433

12

http://www.w3.org/2001/XMLSchema#string

P478

64

http://www.w3.org/2001/XMLSchema#string

P577

2005-12-01T00:00:00Z

http://www.w3.org/2001/XMLSchema#dateTime

P698

16319717

http://www.w3.org/2001/XMLSchema#string