Evaluation of N-nonyl-deoxygalactonojirimycin as a pharmacological chaperone for human GM1 gangliosidosis leads to identification of a feline model suitable for testing enzyme enhancement therapy.
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Candidate molecules for chemical chaperone therapy of GM1-gangliosidosis.Ganglioside biochemistryAn intrinsic mechanism of secreted protein aging and turnoverPharmacological chaperones for enzyme enhancement therapy in genetic diseases.Glycomimetic-based pharmacological chaperones for lysosomal storage disorders: lessons from Gaucher, GM1-gangliosidosis and Fabry diseases.N-Alkyl-, 1-C-Alkyl-, and 5-C-Alkyl-1,5-dideoxy-1,5-imino-(L)-ribitols as Galactosidase Inhibitors.Protein misfolding diseases: prospects of pharmacological treatment.A bicyclic 1-deoxygalactonojirimycin derivative as a novel pharmacological chaperone for GM1 gangliosidosis.
P2860
Q34985010-BFF107A3-2DBF-4951-9B28-CC3810F8172DQ35361488-09771057-9522-42E3-9453-E1F8E658B491Q36268471-84E24B32-13CC-4C82-8129-90661A6C6323Q38162958-EAFF2643-B58B-4AD6-8D2B-BCA80AA5DDD5Q38797648-498D5890-AB33-4D49-9E2C-C173949108CEQ38813807-9294396C-1F5E-486A-AC92-ADDE647A0D61Q39410882-CEB04EE4-46C2-428F-9CFE-DF52E41073A2Q41574484-F8A2258C-152F-476C-8194-57462FE773CB
P2860
Evaluation of N-nonyl-deoxygalactonojirimycin as a pharmacological chaperone for human GM1 gangliosidosis leads to identification of a feline model suitable for testing enzyme enhancement therapy.
description
2012 nî lūn-bûn
@nan
2012 թուականի Յունիսին հրատարակուած գիտական յօդուած
@hyw
2012 թվականի հունիսին հրատարակված գիտական հոդված
@hy
2012年の論文
@ja
2012年論文
@yue
2012年論文
@zh-hant
2012年論文
@zh-hk
2012年論文
@zh-mo
2012年論文
@zh-tw
2012年论文
@wuu
name
Evaluation of N-nonyl-deoxygal ...... ng enzyme enhancement therapy.
@ast
Evaluation of N-nonyl-deoxygal ...... ng enzyme enhancement therapy.
@en
Evaluation of N-nonyl-deoxygal ...... ng enzyme enhancement therapy.
@nl
type
label
Evaluation of N-nonyl-deoxygal ...... ng enzyme enhancement therapy.
@ast
Evaluation of N-nonyl-deoxygal ...... ng enzyme enhancement therapy.
@en
Evaluation of N-nonyl-deoxygal ...... ng enzyme enhancement therapy.
@nl
prefLabel
Evaluation of N-nonyl-deoxygal ...... ng enzyme enhancement therapy.
@ast
Evaluation of N-nonyl-deoxygal ...... ng enzyme enhancement therapy.
@en
Evaluation of N-nonyl-deoxygal ...... ng enzyme enhancement therapy.
@nl
P2093
P2860
P1476
Evaluation of N-nonyl-deoxygal ...... ng enzyme enhancement therapy.
@en
P2093
Brigitte A Rigat
Daphne Benedict
Don J Mahuran
Douglas R Martin
Ellen Crushell
John W Callahan
Justin Buttner
Michael B Tropak
P2860
P304
P356
10.1016/J.YMGME.2012.06.007
P577
2012-06-19T00:00:00Z