Defining a link with autosomal-dominant polycystic kidney disease in mice with congenitally low expression of Pkd1
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Autosomal dominant polycystic kidney disease: the last 3 yearsThe Role of G-Protein-Coupled Receptor Proteolysis Site Cleavage of Polycystin-1 in Renal Physiology and Polycystic Kidney DiseaseA polycystin-centric view of cyst formation and disease: the polycystins revisitedPolycystin-1: a master regulator of intersecting cystic pathwaysExperimental therapies and ongoing clinical trials to slow down progression of ADPKDNovel role of ouabain as a cystogenic factor in autosomal dominant polycystic kidney diseasePolycystic kidney disease - where gene dosage countsA genetic interaction network of five genes for human polycystic kidney and liver diseases defines polycystin-1 as the central determinant of cyst formationPkd1 transgenic mice: adult model of polycystic kidney disease with extrarenal and renal phenotypes.Gene expression in early and progression phases of autosomal dominant polycystic kidney diseaseA novel mouse model reveals that polycystin-1 deficiency in ependyma and choroid plexus results in dysfunctional cilia and hydrocephalus.Hepato-renal pathology in pkd2ws25/- mice, an animal model of autosomal dominant polycystic kidney diseaseDeterminants of renal disease variability in ADPKD.Molecular advances in autosomal dominant polycystic kidney disease.Novel targets for the treatment of autosomal dominant polycystic kidney disease.Genetic mechanisms and signaling pathways in autosomal dominant polycystic kidney disease.A missense mutation in PKD1 attenuates the severity of renal diseaseCyst formation and activation of the extracellular regulated kinase pathway after kidney specific inactivation of Pkd1.Treatment strategies and clinical trial design in ADPKDMolecular diagnostics for autosomal dominant polycystic kidney diseaseMolecular pathways and therapies in autosomal-dominant polycystic kidney diseaseScattered Deletion of PKD1 in Kidneys Causes a Cystic Snowball Effect and Recapitulates Polycystic Kidney DiseaseUrinary EGF Receptor Ligand Excretion in Patients with Autosomal Dominant Polycystic Kidney Disease and Response to Tolvaptan.Functional polycystin-1 dosage governs autosomal dominant polycystic kidney disease severity.Biliary and pancreatic dysgenesis in mice harboring a mutation in Pkhd1.Polycystic kidney disease and renal injury repair: common pathways, fluid flow, and the function of polycystin-1.Effect of genotype on the severity and volume progression of polycystic liver disease in autosomal dominant polycystic kidney disease.Pkd1 inactivation induced in adulthood produces focal cystic diseasePolycystic kidney disease and the renal cilium.Differences in the timing and magnitude of Pkd1 gene deletion determine the severity of polycystic kidney disease in an orthologous mouse model of ADPKD.Loss of polycystin-1 causes centrosome amplification and genomic instabilityPkd2 dosage influences cellular repair responses following ischemia-reperfusion injury.Inactivation of Pkd1 in principal cells causes a more severe cystic kidney disease than in intercalated cellsPolycystin-1 interacts with inositol 1,4,5-trisphosphate receptor to modulate intracellular Ca2+ signaling with implications for polycystic kidney disease.Autosomal dominant polycystic kidney disease: recent advances in pathogenesis and potential therapies.Genetics and pathogenesis of autosomal dominant polycystic kidney disease: 20 years on.Cyst growth, polycystins, and primary cilia in autosomal dominant polycystic kidney disease.Whole-Genome Sequencing Coupled to Imputation Discovers Genetic Signals for Anthropometric Traits.Variable Cyst Development in Autosomal Dominant Polycystic Kidney Disease: The Biologic Context.Genome-wide methylation profiling of ADPKD identified epigenetically regulated genes associated with renal cyst development.
P2860
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P2860
Defining a link with autosomal-dominant polycystic kidney disease in mice with congenitally low expression of Pkd1
description
2006 nî lūn-bûn
@nan
2006 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2006 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2006年の論文
@ja
2006年論文
@yue
2006年論文
@zh-hant
2006年論文
@zh-hk
2006年論文
@zh-mo
2006年論文
@zh-tw
2006年论文
@wuu
name
Defining a link with autosomal ...... nitally low expression of Pkd1
@ast
Defining a link with autosomal ...... nitally low expression of Pkd1
@en
type
label
Defining a link with autosomal ...... nitally low expression of Pkd1
@ast
Defining a link with autosomal ...... nitally low expression of Pkd1
@en
prefLabel
Defining a link with autosomal ...... nitally low expression of Pkd1
@ast
Defining a link with autosomal ...... nitally low expression of Pkd1
@en
P2093
P2860
P1476
Defining a link with autosomal ...... nitally low expression of Pkd1
@en
P2093
Chi-Kuang Leo Wang
Ellian Wang
Hsiu-Kuan Lin
Ying-Chih Chi
Yuan-Ta Lin
Yuan-Yow Chiou
P2860
P304
P356
10.2353/AJPATH.2006.050342
P407
P577
2006-01-01T00:00:00Z